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Thu Feb 9 15:58:13 2006

Papers by A Varki
and the papers citing A Varki

Nodes: 8639, Authors: 20639, Journals: 1435, Outer References: 209299, Words: 12888
Collection span: 1977 - 2006
View: Overview. Sorted by date. Page 1 of 87: [  1  2  3  4  5  6  7  8  9  10 ]  11   21   31   41   51   61   71   81 

#LCRNCRNode / Date / Journal / AuthorLCSGCS
10281 1977 [JUN 30] AMERICAN JOURNAL OF OBSTETRICS AND GYNECOLOGY 128 (6): 591-598
GOLDKRAND JW; VARKI A; MCCLURG JE
SURFACE-TENSION OF AMNIOTIC-FLUID LIPID EXTRACTS - PREDICTION OF PULMONARY MATURITY
1818
20292 1977 [JUN 30] OBSTETRICS AND GYNECOLOGY 50 (2): 191-196
GOLDKRAND JW; VARKI A; MCCLURG JE
RAPID PREDICTION OF PULMONARY MATURITY BY AMNIOTIC-FLUID LIPID GLOBULE FORMATION
66
312903 1978 [JUN 30] ACTA OBSTETRICIA ET GYNECOLOGICA SCANDINAVICA : 5-58
TUIMALA R
CLINICAL STUDIES ON LECITHIN-SPHINGOMY RATIO
00
40204 1978 [JUN 30] AMERICAN HEART JOURNAL 96 (5): 680-688
Varki A; ROBY DS; WATTS H; ZATUCHNI J
SERUM MYOGLOBIN IN ACUTE MYOCARDIAL-INFARCTION - CLINICAL-STUDY AND REVIEW OF LITERATURE
4747
51175 1978 [JUN 30] AMERICAN JOURNAL OF CLINICAL PATHOLOGY 69 (5): 514-519
STATLAND BE; SHER G; FREER DE; KRAYBILL EN; SMITH HY; et al.
EVALUATION OF A MODIFIED FOAM STABILITY (FS-50) TEST - ASSAY PERFORMED ON AMNIOTIC-FLUID TO PREDICT FETAL PULMONARY MATURITY
320
61176 1978 [JUN 30] AMERICAN JOURNAL OF OBSTETRICS AND GYNECOLOGY 132 (6): 681-685
ELRAD H; BEYDOUN SN; HAGEN JH; CABALUM MT; AUBRY RH; et al.
FETAL PULMONARY MATURITY AS DETERMINED BY FLUORESCENT POLARIZATION OF AMNIOTIC-FLUID
229
7007 1978 [JUN 30] CLINICAL RESEARCH 26 (3): A265-A265
ROBY DS; Varki A; ZATUCHNI J
SERUM MYOGLOBIN AND ACUTE MYOCARDIAL-INFARCTION
00
8008 1978 [JUN 30] CLINICAL RESEARCH 26 (3): A358-A358
Varki A; FRITZ JL; DAVIS RB
EFFECTS OF CERVICAL DISLOCATION ON COLONY-FORMING CELLS IN MURINE MARROW CULTURE - IMPLICATIONS FOR MECHANISM OF PLURIPOTENTIAL STEM-CELL COMMITMENT
00
90229 1979 [JUN 30] AMERICAN JOURNAL OF MEDICINE 67 (1): 105-112
MAJERUS P; BIELLO D; ASKIN F; VARKI A
FEVER, HEPATIC-LESIONS AND ASCITES
00
100610 1979 [JUN 30] ARCHIVES OF NEUROLOGY 36 (9): 581-582
Varki A; PUTHURAN P
VALUE OF 2ND LUMBAR PUNCTURE IN CONFIRMING A DIAGNOSIS OF ASEPTIC-MENINGITIS - PROSPECTIVE-STUDY
1515
#LCRNCRNode / Date / Journal / AuthorLCSGCS
1115611 1979 [JUN 30] BRITISH JOURNAL OF CLINICAL PHARMACOLOGY 7 (6): 537-543
MACLEAN D
NON-INVASIVE ASSESSMENT OF THE EFFECTS OF DRUGS ON ACUTE MYOCARDIAL INFARCT SIZE IN MAN
00
120812 1979 [JUN 30] CANCER 43 (2): 695-697
Varki A; ARMITAGE JO; FEAGLER JR
TYPHLITIS IN ACUTE-LEUKEMIA - SUCCESSFUL TREATMENT BY EARLY SURGICAL INTERVENTION
8787
1331913 1979 [JUN 30] CLINICAL CHEMISTRY 25 (10): 1770-1773
STATLAND BE; FREER DE
EVALUATION OF 2 ASSAYS OF FUNCTIONAL SURFACTANT IN AMNIOTIC-FLUID - SURFACE-TENSION LOWERING ABILITY AND THE FOAM STABILITY INDEX TEST
19
140714 1979 [JUN 30] EXPERIMENTAL HEMATOLOGY 7 (8): 397-400
Varki A; FRITZ JL; DAVIS RB
EFFECTS OF CERVICAL DISLOCATION ON COLONY-FORMING CELLS IN MURINE MARROW CULTURES
22
1529415 1979 [JUN 30] JOURNAL OF REPRODUCTIVE MEDICINE 23 (5): 227-235
GABBE SG
RECENT ADVANCES IN THE ASSESSMENT OF FETAL MATURITY
14
1612716 1979 [JUN 30] NEW ENGLAND JOURNAL OF MEDICINE 301 (19): 1013-1018
TORDAY J; CARSON L; LAWSON EE
SATURATED PHOSPHATIDYLCHOLINE IN AMNIOTIC-FLUID AND PREDICTION OF THE RESPIRATORY-DISTRESS SYNDROME
3140
1723317 1979 [JUN 30] OBSTETRICS AND GYNECOLOGY 53 (3): 348-353
GOLDKRAND JW; SLATTERY DS
PATTERNS OF PULMONARY MATURATION IN NORMAL AND ABNORMAL PREGNANCY
14
1813318 1979 [JUN 30] OBSTETRICS AND GYNECOLOGY 53 (4): 500-504
DIVERS WA; HEMSELL DL
USE OF ULTRASOUND IN MULTIPLE GESTATIONS
129
1911519 1980 [JUN 30] AMERICAN HEART JOURNAL 99 (2): 149-154
TOMMASO CL; SALZEIDER K; ARIF M; KLUTZ W
SERIAL MYOGLOBIN VS CPK ANALYSIS AS AN INDICATOR OF UNCOMPLICATED MYOCARDIAL-INFARCTION SIZE AND ITS USE IN ASSESSING EARLY INFARCT EXTENSION
1134
202420 1980 [JUN 30] AMERICAN HEART JOURNAL 100 (6): 948-949
GRENADIER E; KEIDAR S; PALANT A
SERUM MYOGLOBIN AS A SENSITIVE INDEX OF MYOCARDIAL-INFARCTION
12
#LCRNCRNode / Date / Journal / AuthorLCSGCS
211321 1980 [JUN 30] AMERICAN HEART JOURNAL 100 (6): 949-950
TOMMASO CL
SERUM MYOGLOBIN AS A SENSITIVE INDEX OF MYOCARDIAL-INFARCTION - REPLY
00
2201822 1980 [JUN 30] AMERICAN JOURNAL OF HEMATOLOGY 8 (1): 81-86
DAVIS HH; VARKI A; HEATON WA; SIEGEL BA
DETECTION OF ACCESSORY SPLEENS WITH INDIUM 111-LABELED AUTOLOGOUS PLATELETS
3030
2311723 1980 [JUN 30] ARCHIVES OF INTERNAL MEDICINE 140 (6): 834-835
RIFKIN GD
NEUTROPENIC ENTEROCOLITIS AND CLOSTRIDIUM-SEPTICUM INFECTION IN PATIENTS WITH AGRANULOCYTOSIS
2263
240124 1980 [JUN 30] ARCHIVES OF NEUROLOGY 37 (9): 603-603
VARKI A; PUTHURAN P
MENINGITIS AND 2ND LUMBAR PUNCTURE
00
250025 1980 [JUN 30] ARCHIVOS DE BIOLOGIA Y MEDICINA EXPERIMENTALES 13 (4): 442-442
KORNFELD S; TABAS I; VARKI A
STUDIES OF PHOSPHORYLATED OLIGOSACCHARIDES - RECOGNITION MARKERS FOR THE TARGETING OF LYSOSOMAL-ENZYMES
00
2601526 1980 [JUN 30] BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS 94 (2): 567-572
REUTER G; VLIEGENTHART JFG; WEMBER M; SCHAUER R; HOWARD RJ
IDENTIFICATION OF 9-O-ACETYL-N-ACETYLNEURAMINIC ACID ON THE SURFACE OF BALB-C MOUSE ERYTHROCYTES
1431
2721227 1980 [JUN 30] BRITISH JOURNAL OF OBSTETRICS AND GYNAECOLOGY 87 (7): 561-564
BAILEY D; FLYNN AM; KELLY J; OCONOR M
ANTEPARTUM FETAL HEART-RATE MONITORING IN MULTIPLE PREGNANCY
019
2812128 1980 [JUN 30] CHIRURGIE PEDIATRIQUE 21 (4): 257-262
SCHMITT M; PREVOT J; OLIVE D; BORDIGONI P
ACUTE ABDOMEN IN CHILDREN UNDERGOING CANCER-THERAPY
00
291529 1980 [JUN 30] JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION 243 (7): 682-683
POKORNEY BH; JONES JM; SHAIKH BS; ABER RC
TYPHLITIS - TREATABLE CAUSE OF RECURRENT SEPTICEMIA
2836
3001930 1980 [JUN 30] JOURNAL OF BIOLOGICAL CHEMISTRY 255 (18): 8398-8401
VARKI A; KORNFELD S
IDENTIFICATION OF A RAT-LIVER ALPHA-N-ACETYLGLUCOSAMINYL PHOSPHODIESTERASE CAPABLE OF REMOVING BLOCKING ALPHA-N-ACETYLGLUCOSAMINE RESIDUES FROM PHOSPHORYLATED HIGH MANNOSE OLIGOSACCHARIDES OF LYSOSOMAL-ENZYMES
133133
#LCRNCRNode / Date / Journal / AuthorLCSGCS
3102331 1980 [JUN 30] JOURNAL OF BIOLOGICAL CHEMISTRY 255 (22): 10847-10858
VARKI A; KORNFELD S
STRUCTURAL STUDIES OF PHOSPHORYLATED HIGH MANNOSE-TYPE OLIGOSACCHARIDES
103103
3201932 1980 [JUN 30] JOURNAL OF EXPERIMENTAL MEDICINE 152 (3): 532-544
VARKI A; KORNFELD S
AN AUTOSOMAL DOMINANT GENE REGULATES THE EXTENT OF 9-0-ACETYLATION OF MURINE ERYTHROCYTE SIALIC ACIDS - A PROBABLE EXPLANATION FOR THE VARIATION IN CAPACITY TO ACTIVATE THE HUMAN ALTERNATE COMPLEMENT PATHWAY
105105
3311833 1980 [JUN 30] KARDIOLOGIYA 20 (7): 72-75
LESHCHINSKY LA; TRUSOV VV; PIMENOV LT; SUDNEVA LI
RADIOIMMUNOASSAY OF MYOGLOBIN CONCENTRATION IN PATIENTS WITH ISCHEMIC-HEART-DISEASE
00
3411234 1980 [JUN 30] POSTGRADUATE MEDICINE 68 (5): 89-&
LEHMAN JA; ARMITAGE JO
SURGICAL INTERVENTION IN COMPLICATIONS OF ACUTE-LEUKEMIA
711
3512335 1980 [JUN 30] PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES 77 (12): 7074-7078
HASILIK A; KLEIN U; WAHEED A; STRECKER G; VONFIGURA K
PHOSPHORYLATED OLIGOSACCHARIDES IN LYSOSOMAL-ENZYMES - IDENTIFICATION OF ALPHA-N-ACETYLGLUCOSAMINE (1) PHOSPHO (6) MANNOSE DIESTER GROUPS
73114
36111736 1980 [JUN 30] TERAPEVTICHESKII ARKHIV 52 (7): 135-143
STAROVEROV II
MYOGLOBIN DETERMINATION FOR DIAGNOSING MYOCARDIAL-INFARCTION
00
3705537 1981 [JUN 30] AMERICAN JOURNAL OF MEDICAL GENETICS 9 (3): 239-253
HONEY NK; MILLER AL; SHOWS TB
THE MUCOLIPIDOSES - IDENTIFICATION BY ABNORMAL ELECTROPHORETIC PATTERNS OF LYSOSOMAL HYDROLASES
918
3822638 1981 [JUN 30] ARCHIVES DES MALADIES DU COEUR ET DES VAISSEAUX 74 (10): 1205-1215
BOUGET J; DAUBERT JC; CATHELINE M; BEAUVERGER Y; BESSON C; et al.
SERUM MYOGLOBIN ESTIMATION IN ACUTE MYOCARDIAL-INFARCTION
12
3914139 1981 [JUN 30] ARCHIVES OF NEUROLOGY 38 (12): 749-753
GEISELER PJ; NELSON KE; LEVIN S
COMMUNITY-ACQUIRED PURULENT-MENINGITIS OF UNKNOWN ETIOLOGY - A CONTINUING PROBLEM
02
4021940 1981 [JUN 30] ARCHIVES OF SURGERY 116 (7): 943-945
IKARD RW
NEUTROPENIC TYPHLITIS IN ADULTS
3647
#LCRNCRNode / Date / Journal / AuthorLCSGCS
4111541 1981 [JUN 30] BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS 98 (3): 761-767
HASILIK A; WAHEED A; VONFIGURA K
ENZYMATIC PHOSPHORYLATION OF LYSOSOMAL-ENZYMES IN THE PRESENCE OF UDP-N-ACETYLGLUCOSAMINE - ABSENCE OF THE ACTIVITY IN I-CELL FIBROBLASTS
204251
4222242 1981 [JUN 30] BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS 103 (1): 292-300
HOOGEVEEN A; DAZZO A; BROSSMER R; GALJAARD H
CORRECTION OF COMBINED BETA-GALACTOSIDASE-NEURAMINIDASE DEFICIENCY IN HUMAN-FIBROBLASTS
543
4313043 1981 [JUN 30] BLUT 43 (6): 355-360
PAWELSKI S; KONOPKA L; ZDZIECHOWSKA H
RECURRENCE OF THROMBOCYTOPENIA IN PATIENTS SPLENECTOMIZED FOR IDIOPATHIC THROMBOCYTOPENIC PURPURA
031
44415944 1981 [JUN 30] CLINICAL CHEMISTRY 27 (10): 1629-1641
FREER DE; STATLAND BE
MEASUREMENT OF AMNIOTIC-FLUID SURFACTANT
149
450045 1981 [JUN 30] CLINICAL RESEARCH 29 (2): A514-A514
VARKI A; REITMAN ML; KORNFELD S
THE ENZYMATIC DEFECT IN I-CELL DISEASE (ML II) AND PSEUDO-HURLER POLYDYSTROPHY (ML-III)
11
4623546 1981 [JUN 30] DIGESTIVE DISEASES AND SCIENCES 26 (11): 1032-1037
DWORKIN B; WINAWER SJ; LIGHTDALE CJ
TYPHLITIS - REPORT OF A CASE WITH LONG-TERM SURVIVAL AND A REVIEW OF THE RECENT LITERATURE
1837
4732247 1981 [JUN 30] EUROPEAN JOURNAL OF BIOCHEMISTRY 121 (1): 125-129
HASILIK A; VONFIGURA K
OLIGOSACCHARIDES IN LYSOSOMAL-ENZYMES - DISTRIBUTION OF HIGH-MANNOSE AND COMPLEX OLIGOSACCHARIDES IN CATHEPSIN D AND BETA-HEXOSAMINIDASE
3289
480548 1981 [JUN 30] HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE 362 (3): 196-197
VONFIGURA K; HASILIK A; WAHEED A
BIOSYNTHESIS OF THE PHOSPHORYLATED RECOGNITION MARKERS IN LYSOSOMAL-ENZYMES
00
490449 1981 [JUN 30] HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE 362 (3): 241-242
WAHEED A; HASILIK A; POHLMANN R; VONFIGURA K
CHARACTERIZATION AND PARTIAL-PURIFICATION OF A GOLGI-ASSOCIATED ALPHA-N-ACETYLGLUCOSAMINYL PHOSPHODIESTERASE
00
5014450 1981 [JUN 30] IMMUNOLOGY TODAY 2 (7): 129-134
BROWN EJ; FRANK MM
COMPLEMENT ACTIVATION
025
#LCRNCRNode / Date / Journal / AuthorLCSGCS
5121651 1981 [JUN 30] JOURNAL OF BIOLOGICAL CHEMISTRY 256 (9): 4150-4152
WAHEED A; POHLMANN R; HASILIK A; VONFIGURA K
SUBCELLULAR LOCATION OF 2 ENZYMES INVOLVED IN THE SYNTHESIS OF PHOSPHORYLATED RECOGNITION MARKERS IN LYSOSOMAL-ENZYMES
6074
5223952 1981 [JUN 30] JOURNAL OF BIOLOGICAL CHEMISTRY 256 (9): 4275-4281
REITMAN ML; KORNFELD S
UDP-N-ACETYLGLUCOSAMINE - GLYCOPROTEIN N-ACETYLGLUCOSAMINE-1-PHOSPHOTRANSFERASE - PROPOSED ENZYME FOR THE PHOSPHORYLATION OF THE HIGH MANNOSE OLIGOSACCHARIDE UNITS OF LYSOSOMAL-ENZYMES
127166
5333053 1981 [JUN 30] JOURNAL OF BIOLOGICAL CHEMISTRY 256 (11): 5717-5721
WAHEED A; HASILIK A; VONFIGURA K
PROCESSING OF THE PHOSPHORYLATED RECOGNITION MARKER IN LYSOSOMAL-ENZYMES - CHARACTERIZATION AND PARTIAL-PURIFICATION OF A MICROSOMAL ALPHA-N-ACETYLGLUCOSAMINYL PHOSPHODIESTERASE
95106
5434254 1981 [JUN 30] JOURNAL OF BIOLOGICAL CHEMISTRY 256 (17): 9352-9362
MILLER AL; KRESS BC; STEIN R; KINNON C; KERN H; et al.
PROPERTIES OF N-ACETYL-BETA-D-HEXOSAMINIDASE FROM ISOLATED NORMAL AND I-CELL LYSOSOMES
3055
5543255 1981 [JUN 30] JOURNAL OF BIOLOGICAL CHEMISTRY 256 (19): 9937-9943
VARKI A; KORNFELD S
PURIFICATION AND CHARACTERIZATION OF RAT-LIVER ALPHA-N-ACETYLGLUCOSAMINYL PHOSPHODIESTERASE
8686
5603356 1981 [JUN 30] JOURNAL OF BIOLOGICAL CHEMISTRY 256 (20): 243-246
PLUMMER TH; TARENTINO AL
FACILE CLEAVAGE OF COMPLEX OLIGOSACCHARIDES FROM GLYCOPEPTIDES BY ALMOND EMULSIN PEPTIDE - N-GLYCOSIDASE
071
5723157 1981 [JUN 30] JOURNAL OF BIOLOGICAL CHEMISTRY 256 (21): 1224-1231
ERICKSON AH; CONNER GE; BLOBEL G
BIOSYNTHESIS OF A LYSOSOMAL-ENZYME - PARTIAL STRUCTURE OF 2 TRANSIENT AND FUNCTIONALLY DISTINCT NH2-TERMINAL SEQUENCES IN CATHEPSIN-D
0160
5863258 1981 [JUN 30] JOURNAL OF BIOLOGICAL CHEMISTRY 256 (23): 1977-1980
REITMAN ML; KORNFELD S
LYSOSOMAL-ENZYME TARGETING - N-ACETYLGLUCOSAMINYLPHOSPHOTRANSFERASE SELECTIVELY PHOSPHORYLATES NATIVE LYSOSOMAL-ENZYMES
72117
5974159 1981 [JUN 30] JOURNAL OF BIOLOGICAL CHEMISTRY 256 (24): 3060-3067
GOLDBERG DE; KORNFELD S
THE PHOSPHORYLATION OF BETA-GLUCURONIDASE OLIGOSACCHARIDES IN MOUSE P388D1 CELLS
054
60115860 1981 [JUN 30] JOURNAL OF CELL BIOLOGY 91 (3): S77-S103
FARQUHAR MG; PALADE GE
THE GOLGI-APPARATUS (COMPLEX) (1954-1981) FROM ARTIFACT TO CENTER STAGE
24625
#LCRNCRNode / Date / Journal / AuthorLCSGCS
6111761 1981 [JUN 30] JOURNAL OF CLINICAL INVESTIGATION 67 (5): 1574-1579
REITMAN ML; VARKI A; KORNFELD S
FIBROBLASTS FROM PATIENTS WITH I-CELL DISEASE AND PSEUDO-HURLER POLYDYSTROPHY ARE DEFICIENT IN URIDINE 5'-DIPHOSPHATE-N-ACETYLGLUCOSAMINE - GLYCOPROTEIN N-ACETYLGLUCOSAMINYLPHOSPHOTRANSFERASE ACTIVITY
240240
6219262 1981 [JUN 30] JOURNAL OF PEDIATRICS 98 (3): 341-354
PIZZO PA
INFECTIOUS COMPLICATIONS IN THE CHILD WITH CANCER .1. PATHO-PHYSIOLOGY OF THE COMPROMISED HOST AND THE INITIAL EVALUATION AND MANAGEMENT OF THE FEBRILE CANCER-PATIENT
0102
6312863 1981 [JUN 30] KARDIOLOGIYA 21 (8): 38-43
LESCHINSKY LA; PIMENOV LT; SUDNEVA LI
THE USE OF NATURAL KALLIKREIN-PROTEASE INHIBITORS (CONTRYKAL, HORDOX) FOR THE TREATMENT OF ACUTE MYOCARDIAL-INFARCTION
00
6426564 1981 [JUN 30] METHODS IN CELL BIOLOGY 23: 191-214
SLY WS; FISCHER HD; GONZALEZNORIEGA A; GRUBB JH; NATOWICZ M
ROLE OF THE 6-PHOSPHOMANNOSYL-ENZYME RECEPTOR IN INTRACELLULAR-TRANSPORT AND ADSORPTIVE PINOCYTOSIS OF LYSOSOMAL-ENZYMES
1049
6511465 1981 [JUN 30] NEOPLASMA 28 (1): 95-102
MOTYCKA K; BALCAROVA A; PEZLAROVA A; JANDOVA A
CHANGES IN HEMATOPOIESIS OF MICE OF THE C3H STRAIN FOLLOWING TRANSPLANTATION OF GARDNER LYMPHOSARCOMA AND INFECTION WITH LDH-VIRUS .3. BLOOD PROTEINS
011
6682966 1981 [JUN 30] PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES 78 (12): 7773-7777
Varki A; REITMAN ML; KORNFELD S
IDENTIFICATION OF A VARIANT OF MUCOLIPIDOSIS-III (PSEUDO HURLER POLYDYSTROPHY) - A CATALYTICALLY ACTIVE N-ACETYLGLUCOSAMINYL-PHOSPHOTRANSFERASE THAT FAILS TO PHOSPHORYLATE LYSOSOMAL-ENZYMES
7272
671567 1981 [JUN 30] RADIOLOGY 138 (1): 29-30
CRONIN TG; CALANDRA JD; DELFAVA RL
TYPHLITIS PRESENTING AS TOXIC CECITIS
45
6838068 1981 [JUN 30] SCIENCE 213 (4513): 1212-1219
ROTHMAN JE
THE GOLGI-APPARATUS - 2 ORGANELLES IN TANDEM
19372
6922269 1981 [JUN 30] ZEITSCHRIFT FUR KARDIOLOGIE 70 (7): 536-539
KAISER H; GRUNDLER U; SCHRADER J; BLANKE H; RENTROP P; et al.
EARLY PREDICTION OF INFARCT SIZE BY SERIAL DETERMINATION OF SERUM MYOGLOBIN
16
7032270 1982 [JUN 30] AMERICAN JOURNAL OF HUMAN GENETICS 34 (4): 611-622
THOMAS GH; MILLER CS; TOOMEY KE; REYNOLDS LW; REITMAN ML; et al.
2 CLONAL CELL-POPULATIONS (MOSAICISM) IN A 46,XY MALE WITH MUCOLIPIDOSIS-II (I-CELL DISEASE) - AN AUTOSOMAL RECESSIVE DISORDER
33
#LCRNCRNode / Date / Journal / AuthorLCSGCS
7193071 1982 [JUN 30] AMERICAN JOURNAL OF HUMAN GENETICS 34 (5): 717-729
VARKI A; REITMAN ML; VANNIER A; KORNFELD S; GRUBB JH; et al.
DEMONSTRATION OF THE HETEROZYGOUS STATE FOR I-CELL DISEASE AND PSEUDO-HURLER POLYDYSTROPHY BY ASSAY OF N-ACETYLGLUCOSAMINYLPHOSPHOTRANSFERASE IN WHITE BLOOD-CELLS AND FIBROBLASTS
3030
7234172 1982 [JUN 30] AMERICAN JOURNAL OF MEDICAL GENETICS 12 (3): 343-353
SHOWS TB; MUELLER OT; HONEY NK; WRIGHT CE; MILLER AL
GENETIC-HETEROGENEITY OF I-CELL DISEASE IS DEMONSTRATED BY COMPLEMENTATION OF LYSOSOMAL-ENZYME PROCESSING MUTANTS
1927
7311373 1982 [JUN 30] ANALYTICAL BIOCHEMISTRY 123 (1): 78-82
SHUKLA AK; SCHOLZ N; REIMERDES EH; SCHAUER R
HIGH-PERFORMANCE LIQUID-CHROMATOGRAPHY OF N,O-ACYLATED SIALIC ACIDS
1330
7429874 1982 [JUN 30] ANNUAL REVIEW OF NEUROSCIENCE 5: 33-56
BRADY RO
INHERITED METABOLIC STORAGE DISORDERS
013
7553475 1982 [JUN 30] ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS 213 (1): 251-257
ROBEY PG; NEUFELD EF
DEFECTIVE PHOSPHORYLATION AND PROCESSING OF BETA-HEXOSAMINIDASE BY INTACT CULTURED FIBROBLASTS FROM PATIENTS WITH MUCOLIPIDOSIS-III
014
7611676 1982 [JUN 30] ARTHRITIS AND RHEUMATISM 25 (12): 1419-1424
BOMBARDIERI S; CLERICO A; RIENTE L; DELCHICCA MG; VITALI C
CIRCADIAN VARIATIONS OF SERUM MYOGLOBIN LEVELS IN NORMAL SUBJECTS AND PATIENTS WITH POLYMYOSITIS
113
7752477 1982 [JUN 30] BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS 105 (3): 814-820
OWADA M; NEUFELD EF
IS THERE A MECHANISM FOR INTRODUCING ACID-HYDROLASES INTO LIVER LYSOSOMES THAT IS INDEPENDENT OF MANNOSE 6-PHOSPHATE RECOGNITION - EVIDENCE FROM I-CELL DISEASE
60137
7882978 1982 [JUN 30] BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS 105 (3): 1052-1058
WAHEED A; POHLMANN R; HASILIK A; VONFIGURA K; VANELSEN A; et al.
DEFICIENCY OF UDP-N-ACETYLGLUCOSAMINE - LYSOSOMAL-ENZYME N-ACETYLGLUCOSAMINE-1-PHOSPHOTRANSFERASE IN ORGANS OF I-CELL PATIENTS
61116
7922979 1982 [JUN 30] BIOCHEMICAL JOURNAL 202 (1): 183-190
WILLIAMS JC; WEINSTEIN DB; MILLER AL; STEINBERG D
DEFECTIVE CATABOLISM OF LOW-DENSITY LIPOPROTEIN BY FIBROBLASTS FROM PATIENTS WITH I-CELL DISEASE
15
8034080 1982 [JUN 30] BIOCHEMICAL JOURNAL 204 (2): 557-563
HIRANI S; LITTLE L; MILLER AL
A STUDY OF HIGHLY PURIFIED MUCOLIPIDOSIS-III URINARY N-ACETYL-BETA-D-HEXOSAMINIDASE-B
26
#LCRNCRNode / Date / Journal / AuthorLCSGCS
8163281 1982 [JUN 30] BIOCHEMICAL JOURNAL 207 (3): 421-428
KRESS BC; HIRANI S; FREEZE HH; LITTLE L; MILLER AL
MUCOLIPIDOSIS-III BETA-N-ACETYL-D-HEXOSAMINIDASE-A - PURIFICATION AND PROPERTIES
414
8222982 1982 [JUN 30] BIOCHEMICAL JOURNAL 208 (3): 559-566
VLADUTIU GD
THE EFFECT OF CHLOROQUINE ON THE DISTRIBUTION OF NEWLY SYNTHESIZED AND OLD BETA-HEXOSAMINIDASE IN FIBROBLASTS
515
8354083 1982 [JUN 30] BIOCHEMISTRY 21 (19): 4810-4818
PRAKASH C; VIJAY IK
CHARACTERIZATION OF INTERMEDIATES UP TO LIPID-LINKED HEPTASACCHARIDE IMPLICATED IN THE BIOSYNTHESIS OF SACCHAROMYCES-CEREVISIAE MANNOPROTEINS
017
84223884 1982 [JUN 30] BIOCHIMICA ET BIOPHYSICA ACTA 650 (4): 209-232
OLDEN K; PARENT JB; WHITE SL
CARBOHYDRATE MOIETIES OF GLYCOPROTEINS - A RE-EVALUATION OF THEIR FUNCTION
32441
8533585 1982 [JUN 30] BIOCHIMICA ET BIOPHYSICA ACTA 706 (2): 212-220
BEAUREGARD G; MELANCON SB; DALLAIRE L; POTIER M
STUDIES ON SIALIDOSIS AND MUCOLIPIDOSIS - PROPERTIES OF NEURAMINIDASE IN CULTURED SKIN FIBROBLASTS
02
8665386 1982 [JUN 30] BIOCHIMICA ET BIOPHYSICA ACTA 708 (2): 124-133
ALVARES K; BALASUBRAMANIAN AS
LYSOSOMAL AND MICROSOMAL BETA-GLUCURONIDASE OF MONKEY BRAIN DIFFERENTIAL ELUTION CHARACTERISTICS FROM CON A-SEPHAROSE AND NEUTRAL SUGAR COMPOSITION
517
8705087 1982 [JUN 30] BIOCHIMICA ET BIOPHYSICA ACTA 717 (3): 491-501
GEYER R; GEYER H; HUNSMANN G; SCHNEIDER J; STIRM S
SEPARATION PROCEDURE AND SUGAR COMPOSITION OF OLIGOSACCHARIDES IN THE SURFACE GLYCOPROTEIN OF FRIEND MURINE LEUKEMIA-VIRUS
222
8811788 1982 [JUN 30] BIOLOGY OF THE CELL 45: 369-369
HASILIK A; GIESELMANN V; POHLMANN R; STECKEL F; VONFIGURA K
BIOSYNTHESIS OF LYSOSOMAL-ENZYMES
00
8934889 1982 [JUN 30] BIRTH DEFECTS-ORIGINAL ARTICLE SERIES 18 (3B): 3-12
LEROY JG
THE OLIGOSACCHARIDOSES - PROPOSAL OF A NEW NAME AND A NEW CLASSIFICATION FOR THE MUCOLIPIDOSES
02
9041690 1982 [JUN 30] BIRTH DEFECTS-ORIGINAL ARTICLE SERIES 18 (6): 405-409
WOLFE LS
CHEMICAL PATHOLOGY OF THE SIALIDOSES
04
#LCRNCRNode / Date / Journal / AuthorLCSGCS
9113091 1982 [JUN 30] BRITISH HEART JOURNAL 47 (4): 353-356
MCCOMB JM; MCMASTER EA
SERUM MYOGLOBIN AFTER CARDIAC-CATHETERIZATION
04
9211592 1982 [JUN 30] BRITISH JOURNAL OF SURGERY 69 (12): 731-733
MACKINNON AE; HANN IM; MORRISJONES P
CHILDHOOD LEUKEMIA AND SURGERY
12
9315693 1982 [JUN 30] CANADIAN MEDICAL ASSOCIATION JOURNAL 127 (11): 1097-1102
THIVIERGE B; DELAGE G
INFECTIONS OF THE CENTRAL NERVOUS-SYSTEM BY ENTEROVIRUS - 223 CASES SEEN AT A PEDIATRIC HOSPITAL BETWEEN 1973 AND 1981
05
9412894 1982 [JUN 30] CARBOHYDRATE RESEARCH 110 (1): C1-C4
OGAWA T; SETA A
SYNTHETIC STUDIES ON CELL-SURFACE GLYCANS .21. AN APPROACH TO THE SYNTHESIS OF ALDOSYL PHOSPHATES VIA ALDOSYL PHOSPHITES
114
951895 1982 [JUN 30] CHRONOBIOLOGIA 9 (1): 41-45
CLERICO A; PILO A; DELCHICCA MG; RIENTE L; BOMBARDIERI S
CIRCADIAN-RHYTHM OF MYOGLOBIN SERUM CONCENTRATIONS IN HEALTHY-SUBJECTS DEMONSTRATED BY COSINOR ANALYSIS
06
96104796 1982 [JUN 30] CIBA FOUNDATION SYMPOSIA 92: 138-156
KORNFELD S; REITMAN ML; VARKI A; GOLDBERG D; GABEL CA
STEPS IN THE PHOSPHORYLATION OF THE HIGH MANNOSE OLIGOSACCHARIDES OF LYSOSOMAL-ENZYMES
2020
9712897 1982 [JUN 30] CIRCULATION 65 (7): 1522-1528
KLOCKE FJ; COPLEY DP; KRAWCZYK JA; REICHLIN M
RAPID RENAL CLEARANCE OF IMMUNOREACTIVE CANINE PLASMA MYOGLOBIN
937
9811798 1982 [JUN 30] CLINICA CHIMICA ACTA 120 (1): 77-86
HOPWOOD JJ; ELLIOTT H
DETECTION OF THE SANFILIPPO TYPE-B SYNDROME USING RADIOLABELED OLIGOSACCHARIDES AS SUBSTRATES FOR THE ESTIMATION OF ALPHA-N-ACETYLGLUCOSAMINIDASE
113
9921499 1982 [JUN 30] CLINICA CHIMICA ACTA 122 (2): 135-143
DINATALE P; MURINO P; PONTARELLI G; SALVATORE D; ANDRIA G
SANFILIPPO-B SYNDROME (MPS-III-B) - ALTERED RESIDUAL ALPHA-N-ACETYLGLUCOSAMINIDASE ACTIVITY IN AN UNUSUAL SIBSHIP
07
100228100 1982 [JUN 30] CLINICA CHIMICA ACTA 123 (3): 233-240
BENYOSEPH Y; MOMOI T; BAYLERIAN MS; NADLER HL
KM DEFECT IN NEURAMINIDASE OF DYSMORPHIC TYPE SIALIDOSIS WITH AND WITHOUT BETA-GALACTOSIDASE DEFICIENCY
24

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