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Mon Apr 4 11:23:44 2005
Papers from 1995-2005 with one of the following phrases in the title:
fragile x or FMRP or trinucleotitde expansion or nucleotide expansion or cgg

Nodes: 1364, Authors: 3358, Journals: 307, Outer References: 11901, Words: 2507
Collection span: 1995 - 2005
View: Overview. Sorted by date.
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#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
104353 1995 JAN [15] ARCHIVES OF DISEASE IN CHILDHOOD 72(1):3-5
TURK J
FRAGILE-X SYNDROME
24
203054 1995 JAN [15] ARCHIVES OF DISEASE IN CHILDHOOD 72(1):33-37
SLANEY SF; WILKIE AOM; HIRST MC; CHARLTON R; MCKINLEY M; et al.
DNA TESTING FOR FRAGILE-X SYNDROME IN SCHOOLS FOR LEARNING-DIFFICULTIES
1321
3049113 1995 JAN [15] HUMAN MOLECULAR GENETICS 4(1):45-49
DEGRAAFF E; ROUILLARD P; WILLEMS PJ; SMITS APT; ROUSSEAU F; et al.
HOTSPOT FOR DELETIONS IN THE CGG REPEAT REGION OF FMR1 IN FRAGILE-X PATIENTS
3146
4021155 1995 WIN [JAN 15] PSYCHIATRIC GENETICS 5(4):157-160
Jonsson E; Bjorck E; Wahlstrom J; Gustavsson P; Sedvall G
Screening for CGG trinucleotide repeat expansion in the fragile X mental retardation 1 gene in schizophrenic patients
01
50170 1995 JAN 21 BRITISH MEDICAL JOURNAL 310(6973):148-148
CRAFT N
STUDY SUPPORTS SCREENING FOR THE FRAGILE-X-SYNDROME
23
601342 1995 JAN 30 AMERICAN JOURNAL OF MEDICAL GENETICS 55(3):384-386
PRIOR TW; PAPP AC; SNYDER PJ; SEDRA MS; GUIDA M; et al.
GERMLINE MOSAICISM AT THE FRAGILE-X LOCUS
27
700128 1995 FEB [15] JOURNAL OF MEDICAL GENETICS 32(2):144-145
MORTON JE; RINDL PM; BULLOCK S; BUNDEY S; WEBB T
FRAGILE-X SYNDROME IS LESS COMMON THAN PREVIOUSLY ESTIMATED
22
800129 1995 FEB [15] JOURNAL OF MEDICAL GENETICS 32(2):153-153
WANG Q; GREEN EP; BOBROW M; MATHEW CG
SCREENING FOR THE FRAGILE-X A-MUTATION AND E-MUTATION BY AUTOMATED FLUORESCENT ANALYSIS
00
900130 1995 FEB [15] JOURNAL OF MEDICAL GENETICS 32(2):153-153
BULLOCK S; LINDLEY VH; STEVENSON K; COLE T
MOLECULAR DNA TESTING OF A FAMILY MANIFESTING FRAGILE-X SYNDROME IN BOTH THE FRAX-A FULL MUTATION AND MOSAIC FORMS
00
1000131 1995 FEB [15] JOURNAL OF MEDICAL GENETICS 32(2):154-154
BULLOCK S; FELIX CA; BUTTERWORTH MA; STEVENSON K; WILLIAMS D
THE USE OF MOLECULAR DNA TESTING TO DISTINGUISH BETWEEN MUTATIONS AT THE FRAGILE-X A-SITES AND E-SITES
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
11070156 1995 FEB [15] SEMINARS IN CELL BIOLOGY 6(1):5-11
NELSON DL
THE FRAGILE-X SYNDROMES
416
1202847 1995 FEB 27 AMERICAN JOURNAL OF MEDICAL GENETICS 60(1):39-43
SPINELLI M; ROCHA ACD; GIACHETI CM; RICHIERICOSTA A
WORD-FINDING DIFFICULTIES, VERBAL PARAPHASIAS, AND VERBAL DYSPRAXIA IN 10 INDIVIDUALS WITH FRAGILE-X-SYNDROME
77
1300123 1995 MAR 10 JOURNAL OF CELLULAR BIOCHEMISTRY :373-373
WILLEMS PJ; BAKKER CE; REYNIERS E; VERHEIJ C; DEBOULLE K; et al.
A TRANSGENIC MOUSE MODEL FOR FRAGILE-X SYNDROME
00
14020132 1995 MAR [15] JOURNAL OF MEDICAL GENETICS 32(3):170-173
WANG Q; GREEN E; BOBROW M; MATHEW CG
A RAPID, NONRADIOACTIVE SCREENING-TEST FOR FRAGILE-X MUTATIONS AT THE FRAXA AND FRAXE LOCI
1728
15027133 1995 MAR [15] JOURNAL OF MEDICAL GENETICS 32(3):236-239
MACPHERSON JN; CURTIS G; CROLLA JA; DENNIS N; MIGEON B; et al.
UNUSUAL (CGG)(N) EXPANSION AND RECOMBINATION IN A FAMILY WITH FRAGILE-X AND DIGEORGE-SYNDROME
511
1600122 1995 APR 2 JOURNAL OF CELLULAR BIOCHEMISTRY :100-100
MCMURRAY CT; GACY AM; GOELLNER G
HAIRPIN STABILITY DETERMINES THE THRESHOLD AND POTENTIAL FOR NUCLEOTIDE EXPANSION ASSOCIATED WITH HUMAN NEURODEGENERATIVE DISEASE
00
1702450 1995 APR [15] AMERICAN JOURNAL OF OBSTETRICS AND GYNECOLOGY 172(4):1236-1239
RYYNANEN M; KIRKINEN P; MANNERMAA A; SAARIKOSKI S
CARRIER DIAGNOSIS OF THE FRAGILE-X SYNDROME - A CHALLENGE IN ANTENATAL CLINICS
68
18022118 1995 APR [15] JOURNAL OF BACTERIOLOGY 177(7):1915-1917
FUTO S; SETO Y; MITSUSE S; MORI Y; SUZUKI T; et al.
MOLECULAR-CLONING OF A 46-KILODALTON SURFACE-ANTIGEN (P46) GENE FROM MYCOPLASMA-HYOPNEUMONIAE - DIRECT EVIDENCE OF CGG CODON USAGE FOR ARGININE
09
1900104 1995 APR 24 FASEB JOURNAL 9(6):A1324-A1324
SMITH SS; LAAYOUN A; BAKER DJ; KHO MR
RECOGNITION OF TELOMERE-LIKE STRUCTURES FROM THE HUMAN C-HA-RAS GENE AND THE TRINUCLEOTIDE REPEAT OF THE FMR-1 GENE OF FRAGILE-X BY HUMAN DNA METHYLTRANSFERASE
00
2000105 1995 APR 24 FASEB JOURNAL 9(6):A1324-A1324
MITAS M; YU A; DILL J; HAWORTH IS
HAIRPIN PROPERTIES OF SINGLE-STRANDED-DNA CONTAINING G+C-RICH TRIPLET REPEATS - (CTG)(15) AND (CGG)(15)
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
210060 1995 MAY 1 BIOLOGICAL PSYCHIATRY 37(9):629-629
REISS AL
FRAGILE-X SYNDROME
00
2209138 1995 MAY 6 LANCET 345(8958):1147-1148
WILLEMSEN R; MOHKAMSING S; DEVRIES B; DEVYS D; VANDENOUWELAND A; et al.
RAPID ANTIBODY-TEST FOR FRAGILE-X SYNDROME
81101
230372 1995 MAY [15] AMERICAN JOURNAL OF HUMAN GENETICS 56(5):1042-1051
QUAN F; ZONANA J; GUNTER K; PETERSON KL; MAGENIS RE; et al.
AN ATYPICAL CASE OF FRAGILE-X SYNDROME CAUSED BY A DELETION THAT INCLUDES THE FMRI GENE
1930
240653 1995 MAY [15] AMERICAN JOURNAL OF HUMAN GENETICS 56(5):1147-1155
FISCH GS; SNOW K; THIBODEAU SN; CHALIFAUX M; HOLDEN JJA; et al.
THE FRAGILE-X PREMUTATION IN CARRIERS AND ITS EFFECT ON MUTATION SIZE IN OFFSPRING
2835
250169 1995 MAY [15] BRITISH JOURNAL OF PSYCHIATRY 166:688-688
COOKE LB
BEHAVIOR AND DEVELOPMENT IN FRAGILE-X SYNDROME - DYKENS,E
00
26011116 1995 MAY [15] ISRAEL JOURNAL OF MEDICAL SCIENCES 31(5):323-325
DAR H; SCHAAP T; BAITOR H; BOROCHOWITZ Z; GELMANKOHAN Z; et al.
ETHNIC DISTRIBUTION OF THE FRAGILE-X SYNDROME IN ISRAEL - EVIDENCE OF FOUNDER CHROMOSOMES()
11
2701124 1995 MAY [15] JOURNAL OF CHILD PSYCHOLOGY AND PSYCHIATRY AND ALLIED DISCIPLINES 36(4):707-707
TURK J
BEHAVIOR AND DEVELOPMENT IN FRAGILE-X SYNDROME - DYKENS,EM, HODAPP,RM, LECKMAN,JF
00
28052152 1995 MAY [15] PEDIATRICS 95(5):744-752
BAUMGARDNER TL; REISS AL; FREUND LS; ABRAMS MT
SPECIFICATION OF THE NEUROBEHAVIORAL PHENOTYPE IN MALES WITH FRAGILE-X SYNDROME
4975
29018154 1995 MAY 23 PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA 92(11):5199-5203
CHEN XA; MARIAPPAN SVS; CATASTI P; RATLIFF R; MOYZIS RK; et al.
HAIRPINS ARE FORMED BY THE SINGLE DNA STRANDS OF THE FRAGILE-X TRIPLET REPEATS - STRUCTURE AND BIOLOGICAL IMPLICATIONS
33161
30001 1995 JUN 1 AMERICAN JOURNAL OF EPIDEMIOLOGY 141(11):S50-S50
DAWSON DV; LACHIEWICZ AM
BEHAVIORAL EPIDEMIOLOGY OF FRAGILE-X SYNDROME IN FEMALE PEDIATRIC POPULATIONS
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
31043100 1995 JUN 1 EMBO JOURNAL 14(11):2401-2408
SIOMI MC; SIOMI H; SAUER WH; SRINIVASAN S; NUSSBAUM RL; et al.
FXR1, AN AUTOSOMAL HOMOLOG OF THE FRAGILE-X MENTAL-RETARDATION GENE
62102
32011259 1995 JUN 9 BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE 1271(2-3):293-303
FLANNERY AV; HIRST MC; KNIGHT SJL; RITCHIE RJ; DAVIES KE
THE FRAGILE-X SYNDROME
25
33034147 1995 JUN 11 NUCLEIC ACIDS RESEARCH 23(11):1876-1881
MITCHELL JE; NEWBURY SF; MCCLELLAN JA
COMPACT STRUCTURES OF D(CNG)(N) OLIGONUCLEOTIDES IN SOLUTION AND THEIR POSSIBLE RELEVANCE TO FRAGILE-X AND RELATED HUMAN GENETIC-DISEASES
631
341555 1995 JUN [15] ARCHIVES OF DISEASE IN CHILDHOOD 72(6):544-544
TURK J
TREATMENT OF FRAGILE-X SYNDROME
00
350067 1995 JUN [15] BRAIN AND COGNITION 28(1):111-111
GRIGSBY J; KAYE K
VARIABLE EXPRESSION OF DEVELOPMENTAL GERSTMANN SIGNS IN FRAGILE-X SYNDROME
00
360068 1995 JUN [15] BRAIN AND COGNITION 28(1):111-112
GRIGSBY J; KAYE K
DISSOCIATIONS IN DEVELOPMENTAL DYSCALCULIA SECONDARY TO FRAGILE-X SYNDROME
00
37012552 1995 [JUN 30] ANNUAL REVIEW OF NEUROSCIENCE 18:77-99
WARREN ST; ASHLEY CT
TRIPLET REPEAT EXPANSION MUTATIONS - THE EXAMPLE OF FRAGILE-X SYNDROME
2658
3801956 1995 [JUN 30] ARCHIVES OF MEDICAL RESEARCH 26:S77-S83
DiazGallardo MY; BarrosNunez P; Diaz CA; Hernandez A; GomezEspinel I; et al.
Molecular characterization of the fragile-X syndrome in the Mexican population
24
3903062 1995 [JUN 30] BIOSPECTROSCOPY 1(4):235-245
CARMONA P; MOLINA M; LASAGABASTER A; ESCOBAR R
DETERMINATION OF THE HYDROGEN-BONDED STRUCTURE OF CGG TRIMERS IN CHLOROFORM SOLUTION BY VIBRATIONAL SPECTROSCOPY
02
400073 1995 [JUN 30] CYTOGENETICS AND CELL GENETICS 69(1-2):116-116
HOWARDPEEBLES PN
IT IS TIME TO ABANDON THE CYTOGENETIC FRAGILE-X TEST
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
4100102 1995 [JUN 30] EPILEPSIA 36:S1-S1
KLUGER G; BOHM I; LAUB MC; WALDENMEIER C; STUHRMANNSPANGENBERG M
EEG IN CHILDREN WITH FRAGILE-X PREMUTATION
00
4200103 1995 [JUN 30] EPILEPSIA 36:S244-S244
SINGH R; SUTHERLAND G; MANSON J
SEIZURES WITH EPILEPTOGENIC EEG PATTERN IN 2 SISTERS WITH FRAGILE X-SYNDROME
00
4304106 1995 [JUN 30] GENETIC COUNSELING 6(2):97-101
BORGHGRAEF M; SWILLEN A; VANDENBERGHE H; FRYNS JP
FRAGILE-X BOYS - EVOLUTION OF THE MENTAL AGE IN CHILDHOOD - PRELIMINARY DATA ON 10 PREPUBERTAL BOYS
00
4409107 1995 [JUN 30] GENETIC COUNSELING 6(3):207-210
ALEMBIK Y; DOTT B; STOLL C
RETT-LIKE SYNDROME IN FRAGILE-X SYNDROME
16
4504108 1995 [JUN 30] GENETIC COUNSELING 6(4):293-296
FRYNS JP
SCREENING FOR THE FRAGILE-X SYNDROME - THE NECESSITY OF INTERNATIONAL GUIDELINES FOR MOLECULAR-GENETICS PREDICTIVE TESTING IN GENERAL
23
46026109 1995 [JUN 30] GENETIC EPIDEMIOLOGY 12(3):279-290
HUGGINS RM; LOESCH DZ
USE OF ROBUST STATISTICAL-METHODS TO DETERMINE THE EFFECT OF FRAGILE-X ON MEANS AND VARIANCE-COMPONENTS OF A QUANTITATIVE TRAIT
12
47059140 1995 [JUN 30] MEDICINA-BUENOS AIRES 55(5):457-466
BANARES VG
UPDATING THE FRAGILE-X SYNDROME
00
480543 1995 JUL 3 AMERICAN JOURNAL OF MEDICAL GENETICS 57(3):508-509
LAXOVA R
FRAGILE-X SCREENING - WHAT IS THE REAL ISSUE
23
4900145 1995 JUL 8 NEW SCIENTIST 147(1985):10-10
WEBB J
QUESTION MARK HANGS OVER FRAGILE-X TEST IN NEWBORNS
00
5002374 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):167-184
Hagerman R; Staley L; Brown WT; Taylor A; Meadow K; et al.
Conference summary: Fourth International Conference on Fragile X and X-linked Mental Retardation sponsored by the National Fragile X Foundation
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
510075 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):185-186
Nommensen D
Report of the Executive Director of the National Fragile X Foundation
00
5217576 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):187-198
Abrams MT; Reiss AL
Quantitative brain imaging studies of fragile X syndrome
23
53013177 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):199-217
Binstock TC
Fragile X and the amygdala: Cognitive, interpersonal, emotional, and neuroendocrine considerations
44
5401678 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):218-222
Musumeci SA; Ferri R; Elia M; DalGracco S; Scuderi C; et al.
Sleep neurophysiology in fragile X patients
23
5502279 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):223-229
King RA; Hagerman R; Houghton M
Ocular findings in fragile X syndrome
11
5603680 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):230-241
Brun C; Obiols JE; Cheema A; OConnor R; Riddle J; et al.
Longitudinal IQ changes in fragile X females
11
5703381 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):242-251
Freund LS; Peebles CD; Aylward E; Reiss AL
Preliminary report on cognitive and adaptive behaviors of preschool-aged males with fragile X
1722
5807582 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):252-269
Cohen IL
Behavioral profiles of autistic and nonautistic fragile X males
1213
5903883 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):270-279
Belser RC; Sudhalter V
Arousal difficulties in males with fragile X syndrome: A preliminary report
2126
6003784 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):280-292
Sobesky WE; Porter D; Pennington BF; Hagerman RJ
Dimensions of shyness in fragile X females
1419
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
6104185 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):293-301
Jenkins EC; Houck GE; Ding XH; Li SY; StarkHouck SL; et al.
An update on fragile X prenatal diagnosis: End of the cytogenetic testing era
11
6212686 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):302-309
Holden JJA; Chalifoux M; Wing M; JulienInalsingh C; Scott E; et al.
Distribution and frequency of FMR1 CGG repeat number in institutionalized developmentally disabled individuals
02
6302187 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):319-326
Wake SA; Robinson H
Assessment of counselling of normal males and normal transmitting male carriers identified in fragile X families
00
6402588 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):327-335
Roy JC; Johnsen J; Breese K; Hagerman R
Fragile X syndrome: What is the impact of diagnosis on families?
36
6503589 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):336-344
Hagerman RJ; Riddle JE; Roberts LS; Breese K; Fulton M
Survey of the efficacy of clonidine in fragile X syndrome
1212
6602390 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):345-352
Rattazzi MC
Protein therapy in fragile X syndrome - A brief overview of principles, potentials and problems
00
670791 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):359-362
Lin JFH
Introduction to fragile X syndrome for parents
00
680092 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):363-366
Glass L
Females with fragile X: A parent's perspective
00
690993 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):370-379
Holden JJA
Workshop for family and friends .1. The fragile X gene and its mutations
00
700094 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):390-395
McConkieRosell A; Robinson H; Wake S; Staley L; Heller K; et al.
Educating extended family members about the inheritance of the fragile X syndrome
01
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
7101895 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):396-404
Mazzocco MMM; Lachiewicz AM; Kovar CG; Freund LS; Baumgardner TL; et al.
Psychological and emotional studies of the fragile X mutation - A workshop summary
00
720896 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):405-407
Holden JJA; Chalifoux M; Wing M; JulienInalsingh C; Lawson JS; et al.
Distribution and frequency of FMR1 CGG repeat numbers in the general population
613
730997 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):408-410
HowardPeebles PN; Maddalena A; Black SH; Levinson G; Bick DP; et al.
Fragile X screening in pediatric and obstetrical patients
22
740098 1995 JUL-DEC [JUL 15] DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):411-416
[Anon]
4th International Fragile X and X-Linked Mental Retardation Conference - Albuquerque, NM, USA, June 8-12, 1994 - Abstracts
00
7505139 1995 JUL 29 LANCET 346(8970):309-310
CONWAY GS; HETTIARACHCHI S; MURRAY A; JACOBS PA
FRAGILE-X PREMUTATIONS IN FAMILIAL PREMATURE OVARIAN FAILURE
2143
7601948 1995 AUG 14 AMERICAN JOURNAL OF MEDICAL GENETICS 60(4):302-306
MUELLER OT; HARTSFIELD JK; AMAR MJA; GALLARDO LA; KOUSSEFF BG
FRAGILE-X SYNDROME - DISCORDANT LEVELS OF CGG REPEAT MOSAICISM IN 2 BROTHERS
25
770514 1995 AUG [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(2):351-361
ZHONG N; YANG WH; DOBKIN C; BROWN WT
FRAGILE-X GENE INSTABILITY - ANCHORING AGGS AND LINKED MICROSATELLITES
5482
7802461 1995 AUG [15] BIOPHYSICAL JOURNAL 69(2):553-558
RAMAKRISHNAN B; SUNDARALINGAM M
CRYSTAL-STRUCTURE OF THE A-DNA DECAMER D(CCIGGCCM(5)CGG) AT 1.6-ANGSTROM SHOWING THE UNEXPECTED WOBBLE I-CENTER-DOT-M(5)C BASE-PAIR
07
79037125 1995 AUG [15] JOURNAL OF CLINICAL AND EXPERIMENTAL NEUROPSYCHOLOGY 17(4):518-528
HINTON VJ; HALPERIN JM; DOBKIN CS; DING XH; BROWN WT; et al.
COGNITIVE AND MOLECULAR ASPECTS OF FRAGILE-X
59
80014126 1995 AUG [15] JOURNAL OF INTELLECTUAL DISABILITY RESEARCH 39:326-330
SIMON EW; RAPPAPORT DA; PAPKA M; WOODRUFFPAK DS
FRAGILE-X AND DOWNS-SYNDROME - ARE THERE SYNDROME-SPECIFIC COGNITIVE PROFILES AT LOW IQ LEVELS
24
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
81124142 1995 AUG [15] NATURE GENETICS 10(4):483-485
LUGENBEEL KA; PEIER AM; CARSON NL; CHUDLEY AE; NELSON DL
INTRAGENIC LOSS OF FUNCTION MUTATIONS DEMONSTRATE THE PRIMARY ROLE OF FMR1 IN FRAGILE-X SYNDROME
3450
8203344 1995 SEP 11 AMERICAN JOURNAL OF MEDICAL GENETICS 58(3):249-256
LOESCH DZ; HUGGINS RM; HOANG NH
GROWTH IN STATURE IN FRAGILE-X FAMILIES - A MIXED LONGITUDINAL-STUDY
1214
831545 1995 SEP [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(3):609-618
DEGRAAFF E; WILLEMSEN R; ZHONG N; DEDIESMULDERS CEM; BROWN WT; et al.
INSTABILITY OF THE CGG REPEAT AND EXPRESSION OF THE FMR1 PROTEIN IN A MALE FRAGILE-X PATIENT WITH A LUNG-TUMOR
2632
840051 1995 SEP [15] ANNALS OF NEUROLOGY 38(3):499-499
BERRYKRAVIS E; CIURLIONIS R
OVEREXPRESSION OF FRAGILE-X GENE (FMR-1) TRANSCRIPTS IN NEURAL CELLS RESULTS IN INCREASED LEVELS OF CYCLIC ADENOSINE-MONOPHOSPHATE PRODUCTION
00
8503964 1995 SEP-OCT [SEP 15] BRAIN & DEVELOPMENT 17(5):317-321
NANBA E; KOHNO Y; MATSUDA A; YANO M; SATO C; et al.
NONRADIOACTIVE DNA DIAGNOSIS FOR THE FRAGILE-X SYNDROME IN MENTALLY-RETARDED JAPANESE MALES
817
860565 1995 SEP-OCT [SEP 15] BRAIN & DEVELOPMENT 17(5):322-322
NAKAHORI Y
THE INCIDENCE OF THE FRAGILE-X SYNDROME IN JAPANESE - COMMENTARY ON NANBAS PAPER
00
870766 1995 SEP-OCT [SEP 15] BRAIN & DEVELOPMENT 17(5):323-323
KONDO I
NONRADIOACTIVE DNA DIAGNOSIS FOR THE FRAGILE-X SYNDROME IN JAPANESE MENTALLY-RETARDED MALES - COMMENT
00
8801699 1995 SEP [15] DIAGNOSTIC MOLECULAR PATHOLOGY 4(3):158-161
NABER SP
MOLECULAR DIAGNOSIS OF FRAGILE-X SYNDROME
00
89033110 1995 SEP [15] HUMAN GENETICS 96(3):323-329
DREESEN JCFM; GERAEDTS JPM; DUMOULIN JCM; EVERS JLH; PIETERS MHEC
RS46(DXS548) GENOTYPING OF REPRODUCTIVE CELLS - APPROACHING PREIMPLANTATION TESTING OF THE FRAGILE-X SYNDROME
27
9005111 1995 SEP [15] HUMAN GENETICS 96(3):369-370
LENCH NJ; THOMPSON J; MARKHAM AF; ROBINSON PA
(CGG) TRINUCLEOTIDE REPEAT POLYMORPHISM IN THE 5'-REGION OF THE HHR6B GENE - THE HUMAN HOMOLOG OF THE YEAST DNA-REPAIR GENE RAD6
01
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
91231114 1995 SEP [15] HUMAN MOLECULAR GENETICS 4(9):1681-1684
QUAN F; GROMPE M; JAKOBS P; POPOVICH BW
SPONTANEOUS DELETION IN THE FMR1 GENE IN A PATIENT WITH FRAGILE-X SYNDROME AND CHERUBISM
914
9200149 1995 SEP [15] PEDIATRIC RESEARCH 38(3):431-431
DEVONDERWEID U; DAVI F; DECORTI C; CRAGNOLIN E; GLAVINA D
CONTINUOUS GASTRIC INFUSION OF GLUCOSE (CGG) IN THE PREVENTION OF HYPOGLYCEMIA IN LBW INFANTS
00
93035153 1995 SEP [15] PRENATAL DIAGNOSIS 15(9):801-807
CASTELLVIBEL S; MILA M; SOLER A; CARRIO A; SANCHEZ A; et al.
PRENATAL-DIAGNOSIS OF FRAGILE-X SYNDROME - (CGG)(N) EXPANSION AND METHYLATION OF CHORIONIC VILLUS SAMPLES
26
94043119 1995 SEP 29 JOURNAL OF BIOLOGICAL CHEMISTRY 270(39):23090-23096
CHEN FM
ACID-FACILITATED SUPRAMOLECULAR ASSEMBLY OF G-QUADRUPLEXES IN D(CGG)(4)
1037
9513258 1995 OCT 3 BIOCHEMISTRY 34(39):12803-12811
MITAS M; YU A; DILL J; HAWORTH IS
THE TRINUCLEOTIDE REPEAT SEQUENCE D(CGG)(15) FORMS A HEAT-STABLE HAIRPIN CONTAINING G(SYN)CENTER-DOT-G(ANTI) BASE-PAIRS
1563
96014146 1995 OCT 13 NEW ZEALAND MEDICAL JOURNAL 108(1009):404-406
NEVILLE L; COCHRANE J; FITZGERALD P; KENNEDY M
FRAGILE-X MENTAL-RETARDATION SYNDROME - DNA DIAGNOSIS AND CARRIER DETECTION IN NEW-ZEALAND FAMILIES
00
97006 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):40-40
FENG Y; EBERHART DE; WARREN ST
THE PROTEIN ABSENT IN FRAGILE-X SYNDROME (FMRP) IS A RIBOSOME-ASSOCIATED PROTEIN
00
98007 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):135-135
STALEYGANE L; FLYNN L; CRONISTERSILVERMAN A; HAGERMAN RJ
EXPANDING THE ROLE OF THE GENETIC COUNSELOR WORKING WITH FRAGILE-X FAMILIES
00
99008 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):152-152
HUGHES MR; HADDAD BR; SUBRAMANIAN S; NASONKIN I; COTA J; et al.
SINGLE-CELL DETECTION OF THE FMR1, HD, AND SCA1 TRINUCLEOTIDE REPEATS - APPLICATION TO PREIMPLANTATION DIAGNOSIS AND INSTABILITY ANALYSIS OF FRAGILE-X SYNDROME, HUNTINGTON DISEASE, AND SPINO-CEREBELLAR ATAXIA TYPE-1
00
100009 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):153-153
BLACK SH; LEVINSON G; HARTON GL; PALMER FT; SISSON ME; et al.
PREIMPLANTATION GENETIC TESTING (PGT) FOR FRAGILE-X (FRAX)
23
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
1010010 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):196-196
EBERHART DE; FENG Y; WARREN ST
IDENTIFICATION OF A CYTOPLASMIC ANCHOR DOMAIN RESPONSIBLE FOR THE SUBCELLULAR-LOCALIZATION OF THE FRAGILE-X MENTAL-RETARDATION PROTEIN, FMRP
00
1020011 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):211-211
NELSON DL; KUNST CB; LUGENBEEL KA; RYDER OA; WARREN ST; et al.
EVOLUTION OF THE CRYPTIC FMR1 CGG REPEAT
00
1030012 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):494-494
GIANGRECO CA; STEELE MW; ASTON CE; CUMMINS JH; WENGER SL
CLINICAL-CRITERIA FOR FRAGILE-X SOUTHERN BLOT DNA DIAGNOSTIC TESTING
00
1040013 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):585-585
WRIGHTTALAMANTE C; CHEEMA A; RIDDLE JE; LUCKEY D; TAYLOR A; et al.
A CONTROLLED-STUDY OF LONGITUDINAL IQ CHANGES IN FEMALES AND MALES WITH FRAGILE-X SYNDROME
00
1050014 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):655-655
JENKINS EC; DOBKIN CS; DING X; LI SY; HOUCK GE; et al.
THRESHOLD CGG REPEAT SIZE FOR FRAGILE SITE EXPRESSION WITHOUT METHYLATION IDENTIFIED IN LYMPHOCYTE, LYMPHOBLASTOID AND CLONAL LYMPHOBLASTOID CULTURES FROM AN FMR1 UNMETHYLATED MOSAIC FULL MUTATION INDIVIDUAL
00
1060015 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):671-671
MARINI T; PFLUEGER S; NABER S; KARPELLS S; NAEEM R
A 5-YEAR EXPERIENCE WITH FRAGILE-X TESTING
00
1070016 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):692-692
RANCHINO B; TARAVATH A; KALICHMAN M; BURTON BB; MCCORQUODALE MM; et al.
SELECTION AGAINST A MARKER CHROMOSOME IN FRAGILE-X-STRESSED CULTURES
00
1080017 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):869-869
WINKELER KA; WARREN ST
VARIATIONS IN THE LENGTH OF THE CGG-REPEAT OF FMR-1 AFFECT GENE-EXPRESSION
00
1090118 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):906-906
ASHLEY AE; MEADOWS KL; SHERMAN SL
TRANSMISSION CHARACTERISTICS OF THE FMR-1 MUTATION IN THE COLLABORATIVE PROSPECTIVE-STUDY OF THE FRAGILE-X SYNDROME
00
1100019 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):913-913
BROWN WT; ZHONG N; KAJANOJA E; SMITS B; CURLEY D; et al.
FRAGILE-X FOUNDER CHROMOSOME EFFECTS AND NEW MUTATIONS
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
1110020 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):919-919
CHIURAZZI P; KOZAK L; GENUARDI M; GIOVANNUCCIUZIELLI ML; BUSSANI C; et al.
FRAGILE-X SYNDROME - ROUNDER CHROMOSOMES IN ITALY
00
1120021 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):965-965
NOLIN SL; GLICKSMAN A; LEWIS FA; YE LL; HOUCK GE; et al.
EVIDENCE FOR A FAMILIAL FACTOR INVOLVED IN CGG REPEAT EXPANSION IN FRAGILE-X SYNDROME
00
1130022 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1088-1088
CURLEY D; ZHONG N; WANG DW; JU W; DOBKIN C; et al.
NEW INTRAGENIC ALU POLYMORPHISMS IN THE FRAGILE-X GENE
00
1140023 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1218-1218
FALIKBORENSTEIN TC; YALON M; SHACHAK L; DAR C; BOROCHOWITZ Z; et al.
LONG UNINTERRUPTED CGG REPEATS WITHIN THE FMR1 GENE - POSSIBLE MECHANISM FOR THE PREVALENCE OF THE FRAGILE-X SYNDROME AMONG TUNISIAN JEWS
00
1150024 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1273-1273
MILA M; CASTELLVIBEL S; BARCELO A; SANCHEZ A; JIMENEZ D; et al.
MUTATIONS IN THE CPG ISLAND OF THE FMR1 GENE - ARE THEY RESPONSIBLE FOR FRAGILE-X SYNDROME
00
1160025 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1300-1300
PULKKINEN L; MANNERMAA A; KAJANOJA E; RYYNANANEN M; SAARIKOSKI S
DELETION IN THE FMR1 GENE IN A FRAGILE-X-MALE
00
1170026 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1344-1344
WILLEMSEN R; BAKKER C; MANDEL JL; DEVRIES B; DEVYS D; et al.
RAPID SCREENING-TEST FOR FRAGILE-X SYNDROME
00
1180027 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1359-1359
BAKKER C; DEGRAAFF E; ZHONG N; WILLEMSEN R; OOSTRA B
INSTABILITY OF THE CGG REPEAT AND EXPRESSION OF FMR1 PROTEIN IN A MALE-PATIENT WITH A LUNG-TUMOR
00
1190028 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1395-1395
HART PS; OLSON SM; CRANDALL K; TARLETON J
FRAGILE-X SYNDROME RESULTING FROM A 400 BASEPAIR DELETION WITHIN THE FMR1 GENE
02
1200029 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1407-1407
JOHNSON JP; CURRY C; MICEK M; LOUIE E; ABRAMS L; et al.
TRANSMISSION OF STABLE AND UNSTABLE PREMUTATIONS FROM GREAT-GRANDMOTHER AND GREAT-GRANDFATHER RESPECTIVELY - LESSONS FOR GENETIC-COUNSELING IN FRAGILE-X SYNDROME FAMILIES
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
1210030 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1603-1603
BUCHANAN JA; KLOCK RJ; DORAN K; KENNEDY D; WYATT P
PRENATAL TEST FOR FRAGILE-X SYNDROME REVEALS APPARENT FMR1 GENE CONTRACTION
00
1220031 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1676-1676
SHAPIRO LR; WILMOT PL; MARINELLO MJ
NONINDUCED FRAGILE-X CHROMOSOMES DETECTED IN ROUTINE AMNIOTIC-FLUID CELL-CULTURE - DETERMINATION OF SIGNIFICANCE
00
1230032 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1705-1705
DEVRIES BBA; VANDENOUWELAND AMW; MOHKAMSING S; HALLEY DJJ; TIBBEN A; et al.
ACCEPTANCE OF SCREENING FOR THE FRAGILE-X SYNDROME AMONG 1878 MENTALLY-RETARDED INDIVIDUALS IN INSTITUTES AND SPECIAL SCHOOLS IN THE NETHERLANDS
00
1240033 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1838-1838
EIGEL A; ZYGULSKA M; DOLSCHEID T; BOGDANOVA N; DWORNICZAK B; et al.
FRAGILE-X PREMUTATION FREQUENCY IN NORTHERN THAILAND
00
1250134 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1914-1914
GOONEWARDENA P; ZHANG J
A SINGLE TUBE NONRADIOACTIVE PCR ASSAY FOR THE DETECTION OF THE FULL SPECTRUM OR FMR1 CGG REPEATS SEEN IN THE NORMAL, CARRIER AND FRAGILE-X SYNDROME INDIVIDUALS
00
1260035 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1921-1921
JOHNSON DB; QUAN F; BUCHANNAN JA; POPOVICH BW
ALLELIC SIZE LADDERS FCR THE ACCURATE SIZING OF TRINUCLEOTIDE REPEATS IN HUNTINGTON DISEASE AND FRAGILE-X SYNDROME
00
1270036 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1941-1941
TSAI MS; CHIEN TY; YANG YL; CHEN HR; HWANG SM
IDENTIFICATION OF THE NUMBER OF THE FRAGILE-X SYNDROME CGG REPEAT USING SILVER STAIN
00
1280037 1995 OCT [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(4):1947-1947
BROWN CA; BRASINGTON CK; GRASS FS
PATERNAL TRANSMISSION OF A FULL MUTATION IN THE FMR1 GENE - IDENTIFICATION OF PATERNAL CGG REPEAT SHES IN MULTIPLE TISSUES
00
1290663 1995 OCT [15] BONE MARROW TRANSPLANTATION 16(4):625-626
MORTON J; ARNOLD L; FLETCHER B; MCCARTHY C; ROWELL J; et al.
ALLOGENEIC BMT FROM A DONOR WITH FRAGILE-X SYNDROME - CYTOGENETIC AND MOLECULAR EVALUATION
00
130040134 1995 OCT [15] JOURNAL OF MEDICAL GENETICS 32(10):764-769
DEVRIES BBA; ROBINSON H; STOLTEDIJKSTRA I; GI CVTP; DIJKSTRA PF; et al.
GENERAL OVERGROWTH IN THE FRAGILE-X SYNDROME - VARIABILITY IN THE PHENOTYPIC-EXPRESSION OF THE FMR1 GENE MUTATION
616
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
131061144 1995 OCT [15] NEUROPSYCHOLOGY 9(4):470-480
MAZZOCCO MMM; FREUND LS; BAUMGARDNER TL; FORMAN L; REISS AL
NEUROPSYCHOLOGICAL AND PSYCHOSOCIAL EFFECTS OF THE FMR-1 FULL MUTATION - CASE-REPORT OF MONOZYGOTIC TWINS DISCORDANT FOR THE FRAGILE-X SYNDROME
56
132025148 1995 OCT 25 NUCLEIC ACIDS RESEARCH 23(20):4202-4209
USDIN K; WOODFORD KJ
CGG REPEATS ASSOCIATED WITH DNA INSTABILITY AND CHROMOSOME FRAGILITY FORM STRUCTURES THAT BLOCK DNA-SYNTHESIS IN-VITRO
22100
133136101 1995 NOV 1 EMBO JOURNAL 14(21):5358-5366
ZHANG Y; OCONNOR JP; SIOMI MC; SRINIVASAN S; DUTRA A; et al.
THE FRAGILE-X MENTAL-RETARDATION SYNDROME PROTEIN INTERACTS WITH NOVEL HOMOLOGS FXR1 AND FXR2
77121
134044120 1995 NOV 10 JOURNAL OF BIOLOGICAL CHEMISTRY 270(45):27014-27021
KANG SM; OHSHIMA K; SHIMIZU M; AMIRHAERI S; WELLS RD
PAUSING OF DNA-SYNTHESIS IN-VITRO AT SPECIFIC LOCI IN CTG AND CGG TRIPLET REPEATS FROM HUMAN HEREDITARY-DISEASE GENES
1696
13512138 1995 NOV [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(5):991-993
SHERMAN SL
THE HIGH PREVALENCE OF FRAGILE-X PREMUTATION CARRIER FEMALES - IS THIS FREQUENCY UNIQUE TO THE FRENCH-CANADIAN POPULATION
914
13604239 1995 NOV [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(5):1006-1018
ROUSSEAU F; ROUILLARD P; MOREL ML; KHANDJIAN EW; MORGAN K
PREVALENCE OF CARRIERS OF PREMUTATION-SIZE ALLELES OF THE FMRI GENE AND IMPLICATIONS FOR THE POPULATION-GENETICS OF THE FRAGILE-X SYNDROME
86114
1370071 1995 NOV [15] CLINICAL CHEMISTRY 41(11):30-30
RADU DN; CHIANG CS
RAPID, NONRADIOACTIVE SOUTHERN BLOT METHOD FOR DETECTING FRAGILE-X MUTATIONS
00
138028112 1995 NOV [15] HUMAN GENETICS 96(5):577-584
ELALEEM AA; BOHM I; TEMTAMY S; ELAWADY M; AWADALLA M; et al.
DIRECT MOLECULAR ANALYSIS OF THE FRAGILE-X SYNDROME IN A SAMPLE OF EGYPTIAN AND GERMAN PATIENTS USING NONRADIOACTIVE PCR AND SOUTHERN BLOT FOLLOWED BY CHEMILUMINESCENT DETECTION
69
139012135 1995 NOV [15] JOURNAL OF MEDICAL GENETICS 32(11):907-908
PINTADO E; DEDIEGO Y; HMADCHA A; CARRASCO M; SIERRA J; et al.
INSTABILITY OF THE CGG REPEAT AT THE FRAXA LOCUS AND VARIABLE PHENOTYPIC-EXPRESSION IN A LARGE FRAGILE-X PEDIGREE
29
14000141 1995 NOV [15] MOLECULAR BIOLOGY OF THE CELL 6:1801-1801
TANEJA KL; NELSON D; SINGER RH
SPATIAL-DISTRIBUTION OF CGG REPEAT SEQUENCES IN NUCLEI OF FRAGILE-X PATIENT CELLS
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
141140143 1995 NOV [15] NATURE GENETICS 11(3):301-308
EICHLER EE; KUNST CB; LUGENBEEL KA; RYDER OA; DAVISON D; et al.
EVOLUTION OF THE CRYPTIC FMR1 CGG REPEAT
1118
1422117150 1995 NOV [15] PEDIATRIC RESEARCH 38(5):629-637
OOSTRA BA; HALLEY DJJ
COMPLEX BEHAVIOR OF SIMPLE REPEATS - THE FRAGILE-X SYNDROME
811
143043151 1995 NOV [15] PEDIATRIC RESEARCH 38(5):638-643
BERRYKRAVIS E; HICAR M; CIURLIONIS R
REDUCED CYCLIC-AMP PRODUCTION IN FRAGILE-X SYNDROME - CYTOGENETIC AND MOLECULAR CORRELATIONS
44
144146121 1995 DEC 1 JOURNAL OF BIOLOGICAL CHEMISTRY 270(48):28970-28977
NADEL Y; WEISMANSHOMER P; FRY M
THE FRAGILE-X SYNDROME SINGLE-STRAND D(CGG)(N) NUCLEOTIDE REPEATS READILY FOLD BACK TO FORM UNIMOLECULAR HAIRPIN STRUCTURES
1750
14502145 1995 DEC 4 AMERICAN JOURNAL OF MEDICAL GENETICS 59(4):426-430
MCCONKIEROSELL A; ROBINSON H; WAKE S; STALEY LW; HELLER K; et al.
DISSEMINATION OF GENETIC RISK INFORMATION TO RELATIVES IN THE FRAGILE-X SYNDROME - GUIDELINES FOR GENETIC COUNSELORS
78
1460946 1995 DEC 4 AMERICAN JOURNAL OF MEDICAL GENETICS 59(4):526-526
SCHIANO CM; DEMB HB; BROWN WT
LACK OF SIGNIFICANT ASSOCIATION BETWEEN SPINA-BIFIDA AND THE FRAGILE-X SYNDROME
00
147267137 1995 DEC 8 JOURNAL OF MOLECULAR BIOLOGY 254(4):638-656
KETTANI A; KUMAR RA; PATEL DJ
SOLUTION STRUCTURE OF A DNA QUADRUPLEX CONTAINING THE FRAGILE-X SYNDROME TRIPLET REPEAT
1598
14802740 1995 DEC [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(6):1408-1413
LOESCH DZ; HUGGINS R; PETROVIC V; SLATER H
EXPANSION OF THE CGG REPEAT IN FRAGILE-X IN THE FMR1 GENE DEPENDS ON THE SEX OF THE OFFSPRING
813
14924241 1995 DEC [15] AMERICAN JOURNAL OF HUMAN GENETICS 57(6):1414-1425
ASHLEY AE; SHERMAN SL
POPULATION-DYNAMICS OF A MEIOTIC MITOTIC EXPANSION MODEL FOR THE FRAGILE-X SYNDROME
1820
15027872 1995 DEC [15] CLINICS IN LABORATORY MEDICINE 15(4):859-&
Brown WT
Perspectives and molecular diagnosis of the fragile X syndrome
22
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
151125115 1995 DEC [15] HUMAN MOLECULAR GENETICS 4(12):2199-2208
EICHLER EE; HAMMOND HA; MACPHERSON JN; WARD PA; NELSON DL
POPULATION SURVEY OF THE HUMAN FMR1 CGG REPEAT SUBSTRUCTURE SUGGESTS BIASED POLARITY FOR THE LOSS OF AGG INTERRUPTIONS
2035
152024117 1995 DEC [15] JOURNAL OF AUTISM AND DEVELOPMENTAL DISORDERS 25(6):655-662
Lenti C; Peruzzi C; Bianchini E
The association between autism and fragile X syndrome: A case report
01
153026127 1995 DEC [15] JOURNAL OF INTELLECTUAL DISABILITY RESEARCH 39:544-553
Butler MG; Pratesi R; VnencakJones CL
Molecular genetic analysis of mentally retarded males with features of the fragile-X syndrome
01
154035136 1995 DEC [15] JOURNAL OF MEDICAL GENETICS 32(12):925-929
KIRCHGESSNER CU; WARREN ST; WILLARD HF
X INACTIVATION OF THE FMR1 FRAGILE-X MENTAL-RETARDATION GENE
513
15509249 1995 DEC 18 AMERICAN JOURNAL OF MEDICAL GENETICS 60(6):480-493
Schapiro MB; Murphy DGM; Hagerman RJ; Azari NP; Alexander GE; et al.
Adult fragile X syndrome: Neuropsychology, brain anatomy, and metabolism
2131
15604257 1995 DEC 26 BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS 217(3):1015-1025
Xing GQ; Zhang LX; Zhang L; Heynen T; Yoshikawa T; et al.
Rat PPAR delta contains a CGG triplet repeat and is prominently expressed in the thalamic nuclei
054
157020158 1996 JAN [15] AMERICAN JOURNAL OF HUMAN GENETICS 58(1):237-239
Antinolo G; Borrego S; Cabeza JC; Sanchez R; Sanchez J; et al.
Reverse mutation in fragile X syndrome
911
15811224 1996 JAN [15] ARCHIVES OF DISEASE IN CHILDHOOD 74(1):88-88
Magnay D; Morritt J; Waterston T
Fragile X syndrome
00
159113226 1996 WIN [JAN 15] ARCHIVES OF MEDICAL RESEARCH 27(4):587-588
Rivera H
Fragile X studies and authorship
15
160027245 1996 JAN-FEB [JAN 15] EUROPEAN JOURNAL OF HUMAN GENETICS 4(1):8-12
Malzac P; Biancalana V; Voelckel MA; Moncla A; Pellissier MC; et al.
Unexpected inheritance of the (CGG)(n) trinucleotide expansion in a fragile X syndrome family
56
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
16100266 1996 JAN [15] JOURNAL OF INVESTIGATIVE MEDICINE 44(1):A119-A119
Merenstein SA; Sobesky WE; Taylor AK; Tran HX; Riddle JE; et al.
Molecular clinical correlations in males with fragile X syndrome.
00
162131281 1996 JAN [15] NATURE GENETICS 12(1):91-93
Khandjian EW; Corbin F; Woerly S; Rousseau F
The fragile X mental retardation protein is associated with ribosomes
70101
163029286 1996 JAN [15] PEDIATRICS 97(1):122-126
Hagerman RJ; Staley LW; OConner R; Lugenbeel K; Nelson D; et al.
Learning-disabled males with a fragile X CGG expansion in the upper premutation size range
2940
16400230 1996 FEB [15] BIOPHYSICAL JOURNAL 70(2):SU496-SU496
Chen X; Mariappan SVS; Ratliff R; Moyzis RK; Smith SS; et al.
The formation and methylation of the ''slippage structures'' in vitro: The molecular basis of the fragile-X syndrome
00
16514261 1996 FEB [15] INTERNATIONAL JOURNAL OF GYNECOLOGY & OBSTETRICS 52(2):209-210
[Anon]
Fragile X syndrome
00
166127283 1996 FEB 15 NUCLEIC ACIDS RESEARCH 24(4):784-792
Mariappan SVS; Catasti P; Chen X; Ratliff R; Moyzis RK; et al.
Solution structures of the individual single strands of the fragile X DNA triplets (GCC)(n)center dot(GGC)(n)
1249
16700285 1996 FEB [15] PEDIATRIC RESEARCH 39(2):371-371
Torrado M; Herrera J; Chertkoff L; Tenembaum S; Bin L; et al.
Diagnosis value of a pediatric clinical score for the diagnosis of the Fragile X Syndrome
00
168028218 1996 FEB 16 AMERICAN JOURNAL OF MEDICAL GENETICS 67(1):77-80
Simon EW; Finucane BM
Facial emotion identification in males with fragile X syndrome
66
169143263 1996 FEB 23 JOURNAL OF BIOLOGICAL CHEMISTRY 271(8):4327-4334
Deissler H; BehnKrappa A; Doerfler W
Purification of nuclear proteins from human HeLa cells that bind specifically to the unstable tandem repeat (CGG), in the human FMR1 gene
1124
170113159 1996 MAR [15] AMERICAN JOURNAL OF HUMAN GENETICS 58(3):641-643
Brown WT; Zhong N; Dobkin C
Positive fragile X microsatellite associations point to a common mechanism of dynamic mutation evolution
712
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
17103235 1996 MAR [15] CHINESE SCIENCE BULLETIN 41(5):436-437
Huang T; Shen Y; Fan Y; Wu GY
Expression of two alternative splicing isoforms of fragile X gene in human placenta
00
172049257 1996 MAR [15] HUMAN MOLECULAR GENETICS 5(3):319-330
Eichler EE; Macpherson JN; Murray A; Jacobs PA; Chakravarti A; et al.
Haplotype and interspersion analysis of the FMR1 CGG repeat identifies two different mutational pathways for the origin of the fragile X syndrome
3251
173026252 1996 APR [15] HUMAN GENETICS 97(4):512-515
Mornet E; Chateau C; Taillandier A; SimonBouy B; Serre JL
Recurrent and unexpected segregation of the FMR1 CGG repeat in a family with fragile X syndrome
68
174213267 1996 APR [15] JOURNAL OF MEDICAL GENETICS 33(4):338-340
Mila M; CastellviBel S; Sanchez A; Lazaro C; Villa M; et al.
Mosaicism for the fragile X syndrome full mutation and deletions within the CGG repeat of the FMR1 gene
1116
175281228 1996 APR 16 BIOCHEMISTRY 35(15):5041-5053
Pearson CE; Sinden RR
Alternative structures in duplex DNA formed within the trinucleotide repeats of the myotonic dystrophy and fragile X loci
491
176243233 1996 APR 19 CELL 85(2):237-245
Musco G; Stier G; Joseph C; Morelli MAC; Nilges M; et al.
Three-dimensional structure and stability of the KH domain: Molecular insights into the fragile X syndrome
22178
17700248 1996 APR 30 FASEB JOURNAL 10(6):D30-D30
Kramer PR; Pearson CE; Sinden RR
Stability of triplet repeats of myotonic dystrophy and fragile X loci in human mutator mismatch repair cell lines.
00
178121160 1996 MAY [15] AMERICAN JOURNAL OF HUMAN GENETICS 58(5):906-913
Knight SJL; Ritchie RJ; Chakrabarti L; Cross G; Taylor GR; et al.
A study of FRAXE in mentally retarded individuals referred for fragile X syndrome (FRAXA) testing in the United Kingdom
1241
17901242 1996 MAY [15] CONTEMPORARY PSYCHOLOGY 41(5):488-489
McGraw KO
Behavior and development in fragile X syndrome - Dykens,EM, Hodapp,RM, Leckman,JF
00
180194243 1996 MAY [15] DEVELOPMENTAL PSYCHOLOGY 32(3):416-424
Hagerman RJ
Biomedical advances in developmental psychology: The case of fragile X syndrome
38
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
181021268 1996 MAY [15] JOURNAL OF MEDICAL GENETICS 33(5):376-378
Wang ZM; Taylor AK; Bridge JA
FMR1 fully expanded mutation with minimal methylation in a high functioning fragile X male
1722
18201279 1996 MAY [15] MICHIGAN LAW REVIEW 94(6):1810-1838
Friedman RD
Statistics and the evaluation of evidence for forensic scientists - Aitken,CGG
03
183177292 1996 MAY [15] SCREENING 4(4):175-192
Meadows KL; Sherman SL
Fragile X syndrome: Examination of issues pertaining to population-based screening
22
184024163 1996 MAY 17 AMERICAN JOURNAL OF MEDICAL GENETICS 63(2):396-400
Giampietro PF; Haas BR; Lipper E; Gutman A; Zellers NJ; et al.
Fragile X syndrome in two siblings with major congenital malformations
01
185544270 1996 MAY 17 JOURNAL OF MOLECULAR BIOLOGY 258(4):614-626
Shimizu M; Gellibolian R; Oostra BA; Wells RD
Cloning, characterization and properties of plasmids containing CGG triplet repeats from the FMR-1 gene
1449
18601231 1996 JUN [15] BRITISH JOURNAL OF DEVELOPMENTAL PSYCHOLOGY 14:247-248
Happe F
Behavior and development in fragile X syndrome - Dykens,EM, Hodapp,RM, Leckman,JF
00
187012232 1996 JUN [15] BRITISH JOURNAL OF HAEMATOLOGY 93(4):841-844
Arjona SN; EloyGarcia J; Gu LH; Smetanina NS; Huisman THJ
The dominant beta-thalassaemia in a Spanish family is due to a frameshift that introduces an extra CGG codon (=arginine) at the 5' end of the second exon
05
18800237 1996 JUN [15] CLINICAL CHEMISTRY 42(6):441-441
Tsongalis GJ; Hodges KA; Adkins S; Silverman LM
Chemiluminescent detection of the CGG trinucleotide repeat expansion in fragile X syndrome.
00
189062251 1996 JUN [15] GIORNALE DI NEUROPSICHIATRIA DELL ETA EVOLUTIVA 16(2):147-154
Veneselli E; Biancheri R; Perrone MV
Neuropsychiatric aspects in the fragile X syndrome
00
190026253 1996 JUN [15] HUMAN GENETICS 97(6):808-812
Haddad LA; MingroniNetto RC; ViannaMorgante AM; Pena SDJ
A PCR-based test suitable for screening for fragile X syndrome among mentally retarded males
916
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
191325258 1996 JUN [15] HUMAN MOLECULAR GENETICS 5(6):809-813
Tamanini F; Meijer N; Verheij C; Willems PJ; Galjaard H; et al.
FMRP is associated to the ribosomes via RNA
4866
192329259 1996 JUN [15] HUMAN MOLECULAR GENETICS 5(6):821-825
Mornet E; Chateau C; Hirst MC; Thepot F; Taillandier A; et al.
Analysis of germline variation at the FMR1 CGG repeat shows variation in the normal-premutated borderline range
615
193029262 1996 JUN [15] JOURNAL OF AUTISM AND DEVELOPMENTAL DISORDERS 26(3):287-301
Dykens E; Ort S; Cohen I; Finucane B; Spiridigliozzi G; et al.
Trajectories and profiles of adaptive behavior in males with fragile X syndrome: Multicenter studies
1923
194119157 1996 [JUN 30] ACTA BIOCHIMICA POLONICA 43(2):383-388
Milewski M; Zygulska M; Bal J; Deelen WH; Obersztyn E; et al.
Analysis of unstable DNA sequence in FRM1 gene in Polish families with fragile X syndrome
00
195974240 1996 [JUN 30] COLD SPRING HARBOR SYMPOSIA ON QUANTITATIVE BIOLOGY 61:679-687
Eberhart DE; Warren ST
The molecular basis of fragile X syndrome
78
196556241 1996 [JUN 30] COLD SPRING HARBOR SYMPOSIA ON QUANTITATIVE BIOLOGY 61:689-697
Liu Q; Siomi H; Siomi MC; Fischer U; Zhang Y; et al.
Molecular characterization of the protein products of the fragile X syndrome gene and the survival of motor neurons gene
210
197144246 1996 [JUN 30] EUROPEAN PSYCHIATRY 11(5):227-232
Barbe B; Franke P; Maier W; Leboyer M
Fragile X syndrome .1. An overview on its genetic mechanism
00
198071247 1996 [JUN 30] EUROPEAN PSYCHIATRY 11(5):233-243
Franke P; Barbe B; Leboyer M; Maier W
Fragile X syndrome .2. Cognitive and behavioral correlates of mutations of the FMR-1 gene
56
19904249 1996 [JUN 30] GENETIC COUNSELING 7(3):227-230
Fryns JP; DHooghe M; Devriendt K
Macrocephaly, hypospadias grade III-IV, and fragile X-like behavior in identical twins without involvement of the FMR-1 gene
00
200414250 1996 [JUN 30] GENETIC COUNSELING 7(4):245-247
Fryns JP
Ovarian function in fragile X carriers
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
20100271 1996 [JUN 30] JOURNAL OF NEUROCHEMISTRY 67:S34-S34
Chen TA; Lu XF; Yi YH; Ho WKK
Analysis of a CGG sequence at the FMR-1 locus in fragile X site by PCR-DGGE method.
00
20200272 1996 [JUN 30] JOURNAL OF NEUROCHEMISTRY 67:S36-S36
Chen TA; Lu XF; Ilo WKK; Yi YH; Chen SQ; et al.
Variation of the CGG repeat in FMR-1 gene in non retarded Chinese population and fragile X syndrome patients
00
203133294 1996 [JUN 30] VARIATION IN THE HUMAN GENOME 197:119-126
Sutherland GR; Richards RI
Unusual inheritance patterns due to dynamic mutation in fragile X syndrome
00
204020295 1996 [JUN 30] VARIATION IN THE HUMAN GENOME 197:126-136
Weiss KM; Sutherland GR; Harper PS; Bodmer W; Bowcock AM; et al.
Unusual inheritance patterns due to dynamic mutation in fragile X syndrome - Discussion
00
20500164 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):1-1
Laing S; Robinson H; Wake S; Wright F; Turner G
Normal males and their role in transmission of the fragile x syndrome.
00
206934165 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):1-14
Tranebjaerg L; Lubs HA; Borghgraef M; Brown WT; Fisch G; et al.
Seventh International Workshop on the Fragile X and X-linked Mental Retardation
24
20700166 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):6-6
Maes B; Borghraef M; Fryns JP
Presentation of a fragile-X screening list.
00
20800167 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):14-14
Malzac P; Biancalana V; Voelckel MA; Moncla A; Pellissier MC; et al.
A rare example of a reverse mutation in a fragile X syndrome family.
00
20900168 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):16-16
Murray A; Conway GS; Jacobs PA
Premature ovarian failure and fragile X.
00
21000169 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):17-17
Oostra BA; Willemsen R; Mandel JL; DeVries B; Devys D
Rapid screening test for fragile X syndrome.
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
21100170 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):18-18
Oostra B; DeGraaf E; Zhong N; Willemsen R
Instability of the CGG repeat and expression of FMR1 protein in a male patient with a lung tumor.
00
21200171 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):19-19
Shen Y; Zhu N; Huang D; Wu GY
Studies on fragile X syndrome in the Chinese.
00
21300172 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):25-25
deVries BBA; vandenOuweland AMW; Mohkamsing S; Halley DJJ; Tibben A; et al.
Acceptance of screening for the fragile X syndrome among 1878 mentally retarded individuals in institutions and special schools in the Netherlands
00
214121173 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):27-30
Carrel L; Willard HF
An assay for X inactivation based on differential methylation at the fragile X locus, FMR1
132
215312174 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):176-180
Perroni L; Grasso M; Argusti A; LoNigro C; Croci GF; et al.
Molecular and cytogenetic analysis of the fragile X syndrome in a series of 453 mentally retarded subjects: A study of 87 families
67
216112175 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):181-183
Spence WC; Black SH; Fallon L; Maddalena A; Cummings E; et al.
Molecular fragile X screening in normal populations
1318
217010176 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):187-190
Grasso M; Perroni L; Colella S; Piombo G; Argusti A; et al.
Prenatal diagnosis of 30 fetuses at risk for fragile X syndrome
12
218424177 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):191-195
Brown WT; Nolin S; Houck G; Ding XH; Glicksman A; et al.
Prenatal diagnosis and carrier screening for fragile X by PCR
2028
219112178 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):196-197
Turner G; Webb T; Wake S; Robinson; H
Prevalence of fragile X syndrome
153235
220111179 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):198-202
Robinson H; Wake S; Wright F; Laing S; Turner G
Informed choice in fragile X syndrome and its effects on prevalence
911
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
2211050180 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):203-208
Chiurazzi P; Macpherson J; Sherman S; Neri G
Significance of linkage disequilibrium between the fragile X locus and its flanking markers
1825
222359181 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):209-215
Chiurazzi P; Genuardi M; Kozak L; GiovannucciUzielli ML; Bussani C; et al.
Fragile X founder chromosomes in Italy: A few initial events and possible explanation for their heterogeneity
1726
223245182 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):220-225
Eichler EE; Nelson DL
Genetic variation and evolutionary stability of the FMR1 CGG repeat in six closed human populations
1418
224543183 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):226-233
Zhong N; Kajanoja E; Smits B; Pietrofesa J; Curley D; et al.
Fragile X founder effects and new mutations in Finland
1426
225020184 1996 JUL 12 AMERICAN JOURNAL OF MEDICAL GENETICS 64(1):234-238
Syrrou M; Patsalis PC; Georgiou I; Hadjimarcou MI; ConstantinouDeltas CD; et al.
Evidence for high-risk haplotypes and (CGG)n expansion in fragile X syndrome in the Hellenic population of Greece and Cyprus
915
226125222 1996 JUL-AUG [JUL 15] ANNALS OF CLINICAL AND LABORATORY SCIENCE 26(4):323-328
Mark HFL; Bier JAB; Scola P
The frequency of chromosomal abnormalities in patients referred for fragile X analysis
14
227357280 1996 JUL [15] MOLECULAR AND CELLULAR BIOLOGY 16(7):3825-3832
Siomi MC; Zhang Y; Siomi H; Dreyfuss G
Specific sequences in the fragile X syndrome protein FMR1 and the FXR proteins mediate their binding to 60S ribosomal subunits and the interactions among them
58109
228145282 1996 JUL [15] NIMHANS JOURNAL 14(3):201-207
Suresh KP; Girimaji SR; Manjunatha KR
Newer genetics in mental retardation .1. Fragile X syndrome and triplet repeat mutations
01
229028289 1996 SUM [JUL 15] PSYCHIATRIC GENETICS 6(2):81-86
Ashworth A; Abusaad I; Walsh C; Nanko S; Murray RM; et al.
Linkage analysis of the fragile X gene FMR-1 and schizophrenia: No evidence for linkage but report of a family with schizophrenia and an unstable triplet repeat
13
230149291 1996 JUL [15] REVISTA MEDICA DE CHILE 124(7):865-872
Jara L; Avendano I; Aspillaga M; Blanco R
Molecular and genetic features of fragile X syndrome. A review
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
231324227 1996 AUG 5 BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS 225(1):27-33
Willemsen R; Bontekoe C; Tamanini F; Galjaard H; Hoogeveen A; et al.
Association of FMRP with ribosomal precursor particles in the nucleolus
2530
232320185 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):241-245
Kooy RF; DHooge R; Reyniers E; Bakker CE; Nagels G; et al.
Transgenic mouse model for the fragile X syndrome
2544
233337186 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):246-251
Godfraind JM; Reyniers E; DeBoulle K; DHooge R; DeDeyn PP; et al.
Long-term potentiation in the hippocampus of fragile X knockout mice
2534
234321187 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):256-260
Sherman SL; Meadows KL; Ashley AE
Examination of factors that influence the expansion of the fragile X mutation in a sample of conceptuses from known carrier females
1316
235428188 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):261-265
Zhong N; Ju WN; Pietrofesa J; Wang DW; Dobkin C; et al.
Fragile X ''gray zone'' alleles: AGG patterns, expansion risks, and associated haplotypes
1527
236021189 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):266-267
Wohrle D; Schwemmle S; Steinbach P
DNA methylation and triplet repeat stability: New proposals addressing actual questions on the CGG repeat of fragile X syndrome
1118
237117190 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):270-273
MingroniNetto RC; Haddad LA; ViannaMorgante AM
The number of CGG repeats of the FMR1 locus in premutated and fully mutated heterozygotes and their offspring: Implications for the origin of mosaicism
56
238013191 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):274-277
Steyaert J; Borghgraef M; Legius E; Fryns JP
Molecular-intelligence correlations in young fragile X males with a mild CGG repeat expansion in the FMR1 gene
1519
239021192 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):278-282
Lachiewicz AM; Spiridigliozzi GA; McConkieRosell A; Burgess D; Feng Y; et al.
A fragile X male with a broad smear on Southern blot analysis representing 100-500 CGG repeats and no methylation at the EagI site of the FMR-1 gene
911
240335193 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):287-292
Brown WT; Houck GE; Ding XH; Zhong N; Nolin S; et al.
Reverse mutations in the fragile X syndrome
1118
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
241220194 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):293-295
Mannermaa A; Pulkkinen L; Kajanoja E; Ryynanen M; Saarikoski S
Deletion in the FMR1 gene in a fragile-X male
99
242224195 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):296-301
Dobkin CS; Nolin SL; Cohen I; Sudhalter V; Bialer MG; et al.
Tissue differences in fragile X mosaics: Mosaicism in blood cells may differ greatly from skin
911
243343196 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):302-308
deGraaff E; deVries BBA; Willemsen R; vanHemel JO; Mohkamsing S; et al.
The fragile X phenotype in a mosaic male with a deletion showing expression of the FMR1 protein in 28% of the cells
1213
244221197 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):309-312
Maddalena A; Yadvish KN; Spence WC; HowardPeebles PN
A fragile X mosaic male with a cryptic full mutation detected in epithelium but not in blood
1316
24509198 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):319-322
Fisch GS; Carpenter N; Maddalena A; Tarleton J; JulienInalsingh C; et al.
Rater reliability of fragile X mutation size estimates: A multilaboratory analysis
55
246031199 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):323-328
Mazzocco MMM; Holden JJA
Neuropsychological profiles of three sisters homozygous for the fragile X premutation
68
247024200 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):329-333
AllinghamHawkins DJ; Brown CA; Babul R; Chitayat D; Krekewich K; et al.
Tissue-specific methylation differences and cognitive function in fragile X premutation females
813
248018201 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):334-339
Franke P; Maier W; Hautzinger M; Weiffenbach O; Gansicke M; et al.
Fragile-X carrier females: Evidence for a distinct psychopathological phenotype?
2332
249129202 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):340-345
Sobesky WE; Taylor AK; Pennington BF; Bennetto L; Porter D; et al.
Molecular/clinical correlations in females with fragile X
3139
250231203 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):350-355
WrightTalamante C; Cheema A; Riddle JE; Luckey DW; Taylor AK; et al.
A controlled study of longitudinal IQ changes in females and males with fragile X syndrome
1416
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
251141204 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):356-361
Fisch GS; Simensen R; Tarleton J; Chalifoux M; Holden JJ; et al.
Longitudinal study of cognitive abilities and adaptive behavior levels in fragile X males: A prospective multicenter analysis
2734
252114205 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):362-364
Fisch GS; Carpenter N; HowardPeebles PN; Maddalena A; Simensen R; et al.
Lack of association between mutation size and cognitive/behavior deficits in fragile X males: A brief report
13
253221206 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):365-369
Cohen IL; Nolin SL; Sudhalter V; Ding XH; Dobkin CS; et al.
Mosaicism for the FMR1 gene influences adaptive skills development in fragile X-affected males
1516
25417207 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):370-372
Partington MW; Moore DY; Turner GM
Confirmation of early menopause in fragile X carriers
2644
25512208 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):376-376
Burgess B; Partington M; Turner G; Robinson H
Normal age of menarche in fragile X syndrome
33
25616209 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):377-377
HowardPeebles PN
Successful pregnancy in a fragile X carrier by donor egg
23
25707210 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):378-381
Wingrove EJ; Norris J; Barton PL; Hagerman R
Experiences and attitudes concerning genetic testing and insurance in a Colorado population: A survey of families diagnosed with fragile X syndrome
09
258118211 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):395-398
Piussan C; Mathieu M; Berquin P; Fryns JP
Fragile X mutation and FG syndrome-like phenotype
14
259019212 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):404-407
Kambouris M; Snow K; Thibodeau S; Bluhm D; Green M; et al.
Segregation of the fragile X mutation from a male with a full mutation: Unusual somatic instability in the FMR-1 locus
13
260120213 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):413-414
Loesch DZ
Fragile X: Clinical associations
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
261325214 1996 AUG 9 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):428-433
Meadows KL; Pettay D; Newman J; Hersey J; Ashley AE; et al.
Survey of the fragile X syndrome and the fragile X E syndrome in a special education needs population
1327
262437223 1996 AUG [15] ARCHIVES DE PEDIATRIE 3(8):814-821
Mornet E; SimonBouy B
Molecular biology of fragile X syndrome: Applications to genetic counselling and molecular diagnosis
34
263255254 1996 AUG [15] HUMAN GENETICS 98(2):151-157
Kramer PR; Pearson CE; Sinden RR
Stability of triplet repeats of myotonic dystrophy and fragile X loci in human mutator mismatch repair cell lines
227
264553260 1996 AUG [15] HUMAN MOLECULAR GENETICS 5(8):1083-1091
Eberhart DE; Malter HE; Feng Y; Warren ST
The fragile X mental retardation protein is a ribonucleoprotein containing both nuclear localization and nuclear export signals
93132
265017287 1996 AUG [15] PEDIATRICS 98(2):297-300
Desposito F; Cho S; Frias JL; Sherman J; Wappner RS; et al.
Health supervision for children with fragile X syndrome
38
26611215 1996 AUG 23 AMERICAN JOURNAL OF MEDICAL GENETICS 64(3):527-527
Syrrou M; Patsalis PC; Georgiou I; Hadjimarcou MI; ConstantinouDeltas CD; et al.
Evidence for high-risk haplotypes and (CGG)n expansion in fragile X syndrome in the Hellenic population of Greece and Cyprus (vol 64, pg 234, 1996)
00
267237161 1996 SEP [15] AMERICAN JOURNAL OF HUMAN GENETICS 59(3):540-546
Vaisanen ML; Haataja R; Leisti L
Decrease in the CGG(n) trinucleotide repeat mutation of the fragile X syndrome to normal size range during paternal transmission
59
26800229 1996 SEP [15] BIOLOGICALS 24(3):210-210
Chehab FF; Wall J; Cai SP
Lessons derived from the clinical molecular diagnosis of cystic fibrosis, thalassaemia, Fragile X and Huntington's disease
00
269033275 1996 SEP [15] KOREAN JOURNAL OF GENETICS 18(3):199-210
Choi SK; Kim HY; Paik YK
Cytogenetic analysis of a Korean family with fragile X syndrome
01
270137264 1996 SEP 20 JOURNAL OF BIOLOGICAL CHEMISTRY 271(38):22937-22940
Wang YH; Griffith J
Methylation of expanded CCG triplet repeat DNA from fragile X syndrome patients enhances nucleosome exclusion
423
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
271027290 1996 SEP 27 PSYCHIATRY RESEARCH 64(2):97-104
Thompson NM; Rogeness GA; McClure E; Clayton R; Johnson C
Influence of depression on cognitive functioning in Fragile X females
16
272439244 1996 OCT 1 EMBO JOURNAL 15(19):5408-5414
Fridell RA; Benson RE; Hua J; Bogerd HP; Cullen BR
A nuclear role for the fragile X mental retardation protein
3567
273050265 1996 OCT 4 JOURNAL OF BIOLOGICAL CHEMISTRY 271(40):24325-24328
Godde JS; Kass SU; Hirst MC; Wolffe AP
Nucleosome assembly on methylated CGG triplet repeats in the Fragile X Mental Retardation gene 1 promoter
541
27414276 1996 OCT 5 LANCET 348(9032):967-968
Willemsen R; Oosterwijk JC; Los FJ; Galjaard H; Oostra BA
Prenatal diagnosis of fragile X syndrome
1116
27501225 1996 FAL [OCT 15] ARCHIVES OF MEDICAL RESEARCH 27(3):427-427
DiazGallardo
Molecular characterization of the fragile-x syndrome in the Mexican population (vol 26, pg S77, 1995)
00
2761195234 1996 OCT [15] CHILD AND ADOLESCENT PSYCHIATRIC CLINICS OF NORTH AMERICA 5(4):895-&
Hagerman RJ
Fragile X syndrome
19
27700236 1996 OCT 15 CIRCULATION 94(8):534-534
Helbecque N; Dallongeville J; Arveiler D; Cambou JP; Evans A; et al.
Relationship between VLDL receptor gene (CGG) repeat polymorphism and plasma apo E containing lipoparticles levels in a sample of European Caucasian men
00
278434255 1996 OCT [15] HUMAN GENETICS 98(4):409-414
Schmucker B; Ballhausen WG; Pfeiffer RA
Mosaicism of a microdeletion of 486 bp involving the CGG repeat of the FMR1 gene due to misalignment of GTT tandem repeats at chi-like elements flanking both breakpoints and a full mutation
512
279213256 1996 OCT [15] HUMAN GENETICS 98(4):419-421
Mila M; CastellviBel S; Gine R; Vazquez C; Badenas C; et al.
A female compound heterozygote (pre-and full mutation) for the CGG FMR1 expansion
46
280014273 1996 OCT [15] JOURNAL OF PEDIATRICS 129(4):611-614
Giangreco CA; Steele MW; Aston CE; Cummins JH; Wenger SL
A simplified six-item checklist for screening for fragile X syndrome in the pediatric population
1122
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
2810138278 1996 OCT [15] MEDICAL HYPOTHESES 47(4):289-298
Fischer KM
Genes for Prader Willi Syndrome Angelman syndrome and fragile X syndrome are homologous, with genetic imprinting and unstable trinucleotide repeats causing mental retardation, autism and aggression
14
28203216 1996 NOV 11 AMERICAN JOURNAL OF MEDICAL GENETICS 65(4):355-356
Seemanova E
Fragile X syndrome in incestuous families
00
28300219 1996 NOV [15] AMERICAN JOURNAL OF PATHOLOGY 149(5):G4-G4
Zehnbauer BA
Fragile X molecular detection in clinical referrals.
00
28400220 1996 NOV [15] AMERICAN JOURNAL OF PATHOLOGY 149(5):G5-G5
Larsen LA; NorgaardPedersen B; Vuust J
Analysis of fragile X CGG repeats in the normal range by PCR amplification and automated capillary electrophoresis.
00
28500221 1996 NOV [15] AMERICAN JOURNAL OF PATHOLOGY 149(5):G6-G6
Pandya A; FerreiraGonzalez A; JacksonCook C; Ware JL; Garrett CT
Evaluation of fragile X CCG locus using PCR and a fluorescent automated DNA sequencer.
00
28600238 1996 NOV [15] CLINICAL CHEMISTRY 42(11):7-7
Hamdan H; Bailey A; Martinez JJ; Fenwick R; Leon JA
Improved amplification and automated detection of trinucleotide repeats in the diagnosis of fragile X syndrome.
00
287014284 1996 NOV [15] PEDIATRIC NEUROLOGY 15(4):358-360
Kluger G; Bohm I; Laub MC; Waldenmaier C
Epilepsy and fragile X gene mutations
612
288535293 1996 NOV [15] SOMATIC CELL AND MOLECULAR GENETICS 22(6):435-441
Eberhart DE; Warren ST
Nuclease sensitivity of permeabilized cells confirms altered chromatin formation at the fragile X locus
715
28911217 1996 DEC 2 AMERICAN JOURNAL OF MEDICAL GENETICS 66(1):118-118
Perroni L; Grasso M; Argusti A; Nigro CL; Croci GF; et al.
Molecular and cytogenetic analysis of the fragile X syndrome in a series of 453 mentally retarded subjects: A study of 87 families (vol 64, pg 176, 1996)
00
290938162 1996 DEC [15] AMERICAN JOURNAL OF HUMAN GENETICS 59(6):1252-1261
Nolin SL; Lewis FA; Ye LL; Houck GE; Glicksman AE; et al.
Familial transmission of the FMR1 CGG repeat
4354
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
291321239 1996 DEC [15] CLINICAL OBSTETRICS AND GYNECOLOGY 39(4):772-782
Finucane B
Should all pregnant women be offered carrier testing for fragile X syndrome?
11
292220269 1996 DEC [15] JOURNAL OF MEDICAL GENETICS 33(12):1007-1010
deVries BBA; Jansen CCAM; Duits AA; Verheij C; Willemsen R; et al.
Variable FMR1 gene methylation of large expansions leads to variable phenotype in three males from one fragile X family
3138
29304274 1996 DEC [15] JOURNAL OF SLEEP RESEARCH 5(4):272-272
Musumeci SA; Ferri R; Elia M; DelGracco S; Scuderi C; et al.
Normal respiratory pattern during sleep in young fragile X-syndrome patients
11
294045277 1996 DEC [15] MEDICAL ANTHROPOLOGY QUARTERLY 10(4):537-550
Nelkin D
The social dynamics of genetic testing: The case of Fragile-X
16
2951063288 1996 DEC [15] PRENATAL DIAGNOSIS 16(13):1199-1211
Sutherland GR; Mulley JC
Fragile X syndrome and Fragile XE mental retardation
39
296029338 1997 JAN 10 AMERICAN JOURNAL OF MEDICAL GENETICS 68(1):62-69
McConkieRosell A; Spiridigliozzi GA; Iafolla T; Tarleton J; Lachiewicz AM
Carrier testing in the fragile X syndrome: Attitudes and opinions of obligate carriers
713
297441304 1997 JAN [15] AMERICAN JOURNAL OF HUMAN GENETICS 60(1):103-112
FalikZaccai TC; Shachak E; Yalon M; Lis Z; Borochowitz Z; et al.
Predisposition to the fragile X syndrome in Jews of Tunisian descent is due to the absence of AGG interruptions on a rare Mediterranean haplotype
1727
298326361 1997 JAN [15] CLINICAL GENETICS 51(1):1-6
Loesch DZ; Petrovic V; Francis DI; Oertel R; Slater H
''Reduction'' of CGG trinucleotide expansion from mother to offspring in seven fragile-X families
47
29909362 1997 JAN [15] CLINICAL GENETICS 51(1):71-74
Behjati F; Mullarkey M; Bergbaum A; Berry AC; Docherty Z
Chromosome deletion 17p11.2 (Smith-Magenis syndrome) in seven new patients, four of whom had been referred for fragile-X investigation
06
300129398 1997 JAN [15] JOURNAL OF MEDICAL GENETICS 34(1):1-5
Morton JE; Bundey S; Webb TP; MacDonald F; Rindl PM; et al.
Fragile X syndrome is less common than previously estimated
2847

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