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Fri Mar 10 15:15:25 2006
Papers with "Dystrophic Epidermolysis Bullosa" in the title

Nodes: 543, Authors: 1177, Journals: 123, Outer References: 2425, Words: 1041
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Collection span: 1952 - 2006
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#LCRNCRNode / Date / Journal / AuthorLCSGCS
1011 1952 [JUN 30] AMA ARCHIVES OF DERMATOLOGY AND SYPHILOLOGY 65 (6): 744-745
DILLAHA CJ
DYSTROPHIC EPIDERMOLYSIS BULLOSA WITH ALOPECIA
01
2002 1957 [JUN 30] ARCHIVES OF DERMATOLOGY 75 (5): 773-773
ROSTENBERG A
DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
3053 1958 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 70 (5): 182-183
WHITTLE CH; LEAHY JA; DAVIS RA
PEMPHIGOID WITH FEATURES OF DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
4004 1963 [JUN 30] ARCHIVES OF DERMATOLOGY 87 (4): 526-&
OWRANDI M
DYSTROPHIC EPIDERMOLYSIS BULLOSA
01
5065 1969 [JUN 30] AMERICAN JOURNAL OF ROENTGENOLOGY RADIUM THERAPY AND NUCLEAR MEDICINE 105 (3): 644-&
EDLAND RW
DYSTROPHIC EPIDERMOLYSIS BULLOSA - TOLERANCE O BED AND RESPONSE OF MULTIFOCAL SQUAMOUS CELL CARCINOMAS TO IONIZING RADIATION - REPORT OF A CASE
413
6086 1972 [JUN 30] ARCHIVES OF DERMATOLOGY 105 (3): 460-&
SEHGAL VN; SANYAL RK
VITAMIN-E THERAPY IN DYSTROPHIC EPIDERMOLYSIS BULLOSA
14
70137 1972 [JUN 30] DERMATOLOGICA 144 (1): 27-&
SEHGAL VN; VADIRAJ SN; BEOHAR PC; REGE VL
DYSTROPHIC EPIDERMOLYSIS BULLOSA IN A FAMILY - RESPONSE TO VITAMIN-E (TOCOPHEROL)
112
8018 1973 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 89: 67-71
CATTELL A; WADDINGT.E
RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
01
9009 1974 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 91: 12-12
FORMAN L; NALLY FF
ORAL ACQUIRED NON-DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
100010 1974 [JUN 30] BRITISH JOURNAL OF PLASTIC SURGERY 27 (2): 176-181
ZAREM HA; PEARSON RW; LEAF N
SURGICAL MANAGEMENT OF HAND DEFORMITIES IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
919
#LCRNCRNode / Date / Journal / AuthorLCSGCS
110011 1974 [JUN 30] CLINICAL ORTHOPAEDICS AND RELATED RESEARCH (105): 302-303
OMER GE
SURGICAL PROBLEMS IN HYPERPLASTIC DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
120012 1974 [JUN 30] DERMATOLOGISCHE MONATSSCHRIFT 160 (3): 247-247
BECKMANN I
HEREDITARY DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
1311313 1977 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 96 (4): 389-392
SEHGAL VN; REGE VL; GHOSH SK; KAMAT SM
DYSTROPHIC EPIDERMOLYSIS BULLOSA - INTERESTING GASTROINTESTINAL MANIFESTATIONS
215
140014 1977 [JUN 30] CLINICAL RESEARCH 25 (3): A461-A461
BAUER EA
ALTERED COLLAGENASE IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
01
1501315 1977 [JUN 30] JOURNAL OF PEDIATRIC SURGERY 12 (2): 221-226
FONKALSRUD EW; AMENT ME
SURGICAL MANAGEMENT OF ESOPHAGEAL STRICTURE DUE TO RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
224
1602616 1977 [JUN 30] PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA 74 (10): 4646-4650
BAUER EA
RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA - EVIDENCE FOR AN ALTERED COLLAGENASE IN FIBROBLAST-CULTURES
2679
170817 1977 [JUN 30] THORAX 32 (6): 697-699
SEHHAT S; AMIRIE SA
ESOPHAGEAL RECONSTRUCTION FOR COMPLETE STENOSIS DUE TO DYSTROPHIC EPIDERMOLYSIS-BULLOSA
14
1812918 1978 [JUN 30] JOURNAL OF EXPERIMENTAL MEDICINE 148 (5): 1378-1387
BAUER EA; EISEN AZ
RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA - EVIDENCE FOR INCREASED COLLAGENASE AS A GENETIC CHARACTERISTIC IN CELL-CULTURE
32114
190419 1978 [JUN 30] TISSUE ANTIGENS 12 (3): 233-235
OZAWA A; MATSUO I; NIIZUMA K; OHKIDO M; NOSE Y; et al.
HLA-ANTIGENS AND DOMINANT DYSTROPHIC EPIDERMOLYSIS BULLOSA IN A FAMILY STUDY
00
200020 1979 [JUN 30] CLINICAL RESEARCH 27 (2): A446-A446
BAUER EA; FIEHLER WK; ESTERLY NB
INCREASED GLYCOSAMINOGLYCAN ACCUMULATION AS A GENETIC TRAIT IN CELL-CULTURE OF ONE VARIETY OF DOMINANT DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
#LCRNCRNode / Date / Journal / AuthorLCSGCS
210021 1979 [JUN 30] DERMATOLOGISCHE MONATSSCHRIFT 165 (2): 148-148
HEIDELBACH U
DYSTROPHIC EPIDERMOLYSIS BULLOSA HEREDITARIA
00
2222222 1979 [JUN 30] JOURNAL OF CLINICAL INVESTIGATION 64 (1): 32-39
BAUER EA; FIEHLER WK; ESTERLY NB
INCREASED GLYCOSAMINOGLYCAN ACCUMULATION AS A GENETIC CHARACTERISTIC IN CELL-CULTURES OF ONE VARIETY OF DOMINANT DYSTROPHIC EPIDERMOLYSIS BULLOSA
629
230023 1980 [JUN 30] CLINICAL RESEARCH 28 (2): A253-A253
VALLE KJ; BAUER EA
ENHANCED BIOSYNTHESIS OF HUMAN-SKIN COLLAGENASE IN FIBROBLAST-CULTURES FROM RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
240124 1980 [JUN 30] CLINICAL RESEARCH 28 (2): A563-A563
BAUER EA; COOPER TW; TUCKER DR; ESTERLY NB
DIPHENYLHYDANTOIN THERAPY OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA - CLINICAL-TRIAL AND PROPOSED MECHANISM OF ACTION
02
2533525 1980 [JUN 30] JOURNAL OF CLINICAL INVESTIGATION 66 (2): 176-187
VALLE KJ; BAUER EA
ENHANCED BIOSYNTHESIS OF HUMAN-SKIN COLLAGENASE IN FIBROBLAST-CULTURES FROM RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
1454
260126 1980 [JUN 30] JOURNAL OF INVESTIGATIVE DERMATOLOGY 74 (4): 261-262
BAUER EA; COOPER TW; TUCKER DR; ESTERLY NB
DIPHENYLHYDANTOIN THERAPY OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA - CLINICAL-TRIAL AND PROPOSED MECHANISM OF ACTION
00
2733727 1980 [JUN 30] NEW ENGLAND JOURNAL OF MEDICINE 303 (14): 776-781
BAUER EA; COOPER TW; TUCKER DR; ESTERLY NB
PHENYTOIN THERAPY OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA - CLINICAL-TRIAL AND PROPOSED MECHANISM OF ACTION ON COLLAGENASE
27145
280028 1980 [JUN 30] NEW ZEALAND MEDICAL JOURNAL 91 (655): 193-193
GREVILLE J
DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
2932629 1981 [JUN 30] ARCHIVES OF DERMATOLOGY 117 (9): 529-530
BAUER EA; COOPER TW
THERAPEUTIC CONSIDERATIONS IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
520
3011430 1981 [JUN 30] CLINICAL PEDIATRICS 20 (8): 493-496
BURKHART CG; RUPPERT ES
DYSTROPHIC EPIDERMOLYSIS BULLOSA
01
#LCRNCRNode / Date / Journal / AuthorLCSGCS
310031 1981 [JUN 30] CLINICAL RESEARCH 29 (2): A286-A286
STRICKLIN GP; BAUER EA
CHARACTERIZATION OF FIBROBLAST COLLAGENASE FROM RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
03
3201032 1982 [JUN 30] DERMATOLOGICA 165 (1): 39-46
CARAPETO FJ; PASTOR JA; MARTIN J; AGURRUZA J
RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA AND MULTIPLE SQUAMOUS-CELL CARCINOMAS
516
3334133 1982 [JUN 30] JOURNAL OF CLINICAL INVESTIGATION 69 (6): 1373-1383
STRICKLIN GP; WELGUS HG; BAUER EA
HUMAN-SKIN COLLAGENASE IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA - PURIFICATION OF A MUTANT ENZYME FROM FIBROBLAST-CULTURES
1140
3432934 1982 [JUN 30] JOURNAL OF INVESTIGATIVE DERMATOLOGY 79: S105-S108
BAUER EA
ABNORMALITIES IN COLLAGENASE EXPRESSION AS INVITRO MARKERS FOR RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
026
3532035 1982 [JUN 30] JOURNAL OF INVESTIGATIVE DERMATOLOGY 79 (3): 208-211
KRONBERGER A; VALLE KJ; EISEN AZ; BAUER EA
ENHANCED CELL-FREE TRANSLATION OF HUMAN-SKIN COLLAGENASE IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
526
361936 1982 [JUN 30] ZEITSCHRIFT FUR KINDERCHIRURGIE-SURGERY IN INFANCY AND CHILDHOOD 35 (3): 118-120
LAMESCH A; REIFFERS J
SURGICAL-TREATMENT OF SYNDACTYLIA IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
11
3732237 1983 [JUN 30] ANAESTHESIA 38 (5): 485-491
TOMLINSON AA
RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA - THE ANESTHETIC MANAGEMENT OF A CASE FOR MAJOR SURGERY
514
381438 1983 [JUN 30] ARCHIVES OF DERMATOLOGY 119 (7): 537-537
ZACKHEIM HS
FAILURE OF HUMAN GROWTH-HORMONE TO BENEFIT DYSTROPHIC EPIDERMOLYSIS BULLOSA
11
390539 1983 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 108 (4): 477-483
WOJNAROWSKA FT; EADY RAJ; WELLS RS
DYSTROPHIC EPIDERMOLYSIS BULLOSA PRESENTING WITH CONGENITAL LOCALIZED ABSENCE OF SKIN - REPORT OF 4 CASES
120
4021640 1983 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 108 (6): 687-694
TAKAMORI K; NAITO K; TANEDA A; OGAWA H
INCREASED NEUTRAL PROTEASE AND COLLAGENASE ACTIVITY IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
1330
#LCRNCRNode / Date / Journal / AuthorLCSGCS
4142741 1983 [JUN 30] COLLAGEN AND RELATED RESEARCH 3 (2): 115-124
CHURCH RL; BAUER EA; EISEN AZ
HUMAN-SKIN COLLAGENASE - ASSIGNMENT OF THE STRUCTURAL GENE TO CHROMOSOME-11 IN BOTH NORMAL AND RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA CELLS USING HUMAN-MOUSE SOMATIC-CELL HYBRIDS
623
420042 1983 [JUN 30] JOURNAL OF CUTANEOUS PATHOLOGY 10 (5): 392-392
NANCHAHAL J; TIDMAN MJ
PERIODATE-LABILE STRUCTURES AT THE DERMO-EPIDERMAL JUNCTION IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
430043 1983 [JUN 30] JOURNAL OF INVESTIGATIVE DERMATOLOGY 80 (4): 342-342
TIDMAN MJ; EADY RAJ
DYSTROPHIC EPIDERMOLYSIS BULLOSA - ULTRASTRUCTURAL MORPHOMETRY OF THE DERMO-EPIDERMAL JUNCTION
16
440444 1983 [JUN 30] JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY 9 (5): 766-766
FRITSCH P; KLEIN G; AUBOCK J; HINTNER H
RETINOID THERAPY OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
06
450245 1983 [JUN 30] JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY 9 (5): 766-767
BAUER EA
RETINOID THERAPY OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA - REPLY
00
460046 1983 [JUN 30] ZEITSCHRIFT FUR HAUTKRANKHEITEN H&G 58 (8): 555-&
WIRTH H; NESCH A; OSTAPOWICZ B; ANTONLAMPRECHT I
PHENYTOIN THERAPY OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA (EPIDERMOLYSIS BULLOSA DYSTROPHICA HALLOPEAU-SIEMENS AND EPIDERMOLYSIS BULLOSA DYSTROPHICA INVERSA)
1015
470547 1984 [JUN 30] ACTA DERMATO-VENEREOLOGICA 64 (3): 253-256
OAKLEY CA; GAWKRODGER DJ; ROSS JA; HUNTER JAA
THE COCKAYNE-TOURAINE TYPE OF DOMINANT DYSTROPHIC EPIDERMOLYSIS BULLOSA - ULTRASTRUCTURAL SIMILARITIES TO THE PASINI VARIANT
01
481348 1984 [JUN 30] ARCHIVES OF DERMATOLOGY 120 (6): 707-708
CHALMERS RJG; SHUSTER S
DOMINANT DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
4913149 1984 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 111 (4): 379-387
TIDMAN MJ; EADY RAJ
EVIDENCE FOR A FUNCTIONAL DEFECT OF THE LAMINA LUCIDA IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA DEMONSTRATED BY SUCTION BLISTERS
617
500050 1984 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 111 (6): 713-714
MEATS J; WEISS JB; MATHERS J; EADY RAJ; TIDMAN MJ; et al.
ENHANCED RESPONSIVENESS OF DYSTROPHIC EPIDERMOLYSIS BULLOSA FIBROBLASTS TO INTERLEUKIN-I
00
#LCRNCRNode / Date / Journal / AuthorLCSGCS
510051 1984 [JUN 30] DERMATOLOGICA 169 (4): 234-234
BAUER EA
INHIBITION OF COLLAGENASE EXPRESSION IN NORMAL AND RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA FIBROBLAST-CULTURES BY RETINOIC ACID
01
5251952 1984 [JUN 30] GASTROENTEROLOGY 87 (6): 1376-1380
FEURLE GE; WEIDAUER H; BALDAUF G; SCHULTEBRAUCKS T; ANTONLAMPRECHT I
MANAGEMENT OF ESOPHAGEAL STENOSIS IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
724
530053 1984 [JUN 30] JOURNAL OF CUTANEOUS PATHOLOGY 11 (3): 228-228
MESQUITAGUIMARAES J
ULTRASTRUCTURE OF THE EPIDERMIS IN SCARRED LESIONS OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
00
540054 1984 [JUN 30] JOURNAL OF INVESTIGATIVE DERMATOLOGY 82 (5): 546-546
NANCHAHAL J; TIDMAN MJ
PERIODATE-LABILE STRUCTURES AT THE DERMOEPIDERMAL JUNCTION IN DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
5511355 1984 [JUN 30] JOURNAL OF THE ROYAL SOCIETY OF MEDICINE 77: 37-39
TIDMAN MJ; ATHERTON DJ; EADY RAJ
SQUAMOUS-CELL CARCINOMA AS A COMPLICATION OF DYSTROPHIC EPIDERMOLYSIS BULLOSA
47
561657 1985 [JUN 30] ARCHIVES OF DERMATOLOGICAL RESEARCH 277 (5): 404-405
WEISMANN K
DYSTROPHIC EPIDERMOLYSIS BULLOSA TREATED UNSUCCESSFULLY WITH ORAL ZINC
12
5702158 1985 [JUN 30] ARCHIVES OF DERMATOLOGY 121 (8): 1014-1017
FINE JD; OSMENT LS; GAY S
DYSTROPHIC EPIDERMOLYSIS BULLOSA - A NEW VARIANT CHARACTERIZED BY PROGRESSIVE SYMMETRICAL CENTRIPETAL INVOLVEMENT WITH SCARRING
24
5821559 1985 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 112 (5): 533-538
TAKAMORI K; IKEDA S; NAITO K; OGAWA H
PROTEASES ARE RESPONSIBLE FOR BLISTER FORMATION IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA AND EPIDERMOLYSIS BULLOSA SIMPLEX
416
590060 1985 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 113: 80-81
TIDMAN MJ; MARSDEN RA
SEVERE DOMINANT DYSTROPHIC EPIDERMOLYSIS BULLOSA
22
600061 1985 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 113: 82-82
TIDMAN MJ; MACDONALD DM; WELLS RS
RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA COMPLICATED BY SQUAMOUS-CELL CARCINOMA
02
#LCRNCRNode / Date / Journal / AuthorLCSGCS
6121562 1985 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 113 (4): 397-404
NANCHAHAL J; TIDMAN MJ
A STUDY OF THE DERMO-EPIDERMAL JUNCTION IN DYSTROPHIC EPIDERMOLYSIS BULLOSA USING THE PERIODIC ACID-THIOSEMICARBAZIDE-SILVER PROTEINATE TECHNIQUE
13
6241963 1985 [JUN 30] BRITISH JOURNAL OF DERMATOLOGY 113 (6): 661-667
IKEDA S; NAITO K; IMAI R; MANABE M; TAKAMORI K; et al.
ORIGIN AND PROPERTIES OF THE BLISTER FORMATION FACTOR IN BLISTER FLUIDS FROM RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
25
6301164 1985 [JUN 30] JOURNAL OF CUTANEOUS PATHOLOGY 12 (2): 130-141
HASHIMOTO K; TAKAHASHI S; FREILICH I
BULLOUS CONGENITAL ICHTHYOSIFORM ERYTHRODERMA MASQUERADING AS DYSTROPHIC EPIDERMOLYSIS BULLOSA
01
6431765 1985 [JUN 30] JOURNAL OF INVESTIGATIVE DERMATOLOGY 84 (5): 374-377
TIDMAN MJ; EADY RAJ
EVALUATION OF ANCHORING FIBRILS AND OTHER COMPONENTS OF THE DERMAL-EPIDERMAL JUNCTION IN DYSTROPHIC EPIDERMOLYSIS BULLOSA BY A QUANTITATIVE ULTRASTRUCTURAL TECHNIQUE
75155
650066 1985 [JUN 30] JOURNAL OF INVESTIGATIVE DERMATOLOGY 84 (5): 448-448
HEAGERTY AHM; KENNEDY AR; LEIGH IM; EADY RAJ
LH 7-2 MONOCLONAL-ANTIBODY DEFINES A COMMON DERMOEPIDERMAL JUNCTION DEFECT IN RECESSIVE FORMS OF DYSTROPHIC EPIDERMOLYSIS BULLOSA
27
6662767 1985 [JUN 30] LARYNGOLOGIE RHINOLOGIE OTOLOGIE VEREINIGT MIT MONATSSCHRIFT FUR OHRENHEILKUNDE 64 (10): 522-526
WEIDAUER H; FEURLE GE; BALDAUF G; ANTONLAMPRECHT I
CONSERVATIVE TREATMENT OF ESOPHAGEAL STRICTURES IN PATIENTS WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
22
6793856 1985 DEC 30 ANNALS OF THE NEW YORK ACADEMY OF SCIENCES 460: 311-320
BAUER EA
COLLAGENASE IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
02
681968 1986 [JUN 30] ANNALES DE DERMATOLOGIE ET DE VENEREOLOGIE 113 (8): 697-700
NAZZARO V; BLANCHETBARDON C; DEROUBAIX P; MIMOZ C; PUISSANT A
DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA WITH CONGENITAL LOCALIZED ABSENCE OF SKIN
01
691169 1986 JUL [15] BRITISH JOURNAL OF DERMATOLOGY 115: 20-20
HEAGERTY AHM; TIDMAN MJ; LEIGH IM; JASSIM A; EADY RAJ
DYSTROPHIC EPIDERMOLYSIS-BULLOSA - MONOCLONAL-ANTIBODIES REVEAL HETEROGENEITY WITHIN CLINICAL GROUPS
01
700070 1986 JUL [15] BRITISH JOURNAL OF DERMATOLOGY 115: 86-86
WOOD ML; HARRINGTON CI
RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
00
#LCRNCRNode / Date / Journal / AuthorLCSGCS
710271 1986 JUL [15] BRITISH JOURNAL OF DERMATOLOGY 115: 86-87
WOOD ML; HARRINGTON CI
DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA (PASINI VARIANT)
00
720074 1986 JUL [15] JOURNAL OF INVESTIGATIVE DERMATOLOGY 87 (1): 128-128
BAUER EA; LUDMAN MD; GOLDBERG JD; BERKOWITZ RL; HOLBROOK KA
COLLAGENASE IN ANTENATAL DIAGNOSIS OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
00
7341772 1986 AUG [15] BRITISH JOURNAL OF DERMATOLOGY 115 (2): 125-131
HEAGERTY AHM; KENNEDY AR; LEIGH IM; PURKIS P; EADY RAJ
IDENTIFICATION OF AN EPIDERMAL BASEMENT-MEMBRANE DEFECT IN RECESSIVE FORMS OF DYSTROPHIC EPIDERMOLYSIS-BULLOSA BY LH 7-2 MONOCLONAL-ANTIBODY - USE IN DIAGNOSIS
60125
7421373 1986 NOV-DEC [NOV 15] CLINICAL PHYSIOLOGY AND BIOCHEMISTRY 4 (6): 350-354
FRANCES C; MEIMON G; HERSON S; ROBERT L
STUDY OF ELASTASE-TYPE ACTIVITY IN BLISTER FLUIDS OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
03
7563975 1986 NOV [15] JOURNAL OF INVESTIGATIVE DERMATOLOGY 87 (5): 597-601
BAUER EA; LUDMAN MD; GOLDBERG JD; BERKOWITZ RL; HOLBROOK KA
ANTENATAL DIAGNOSIS OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA - COLLAGENASE EXPRESSION IN CULTURED FIBROBLASTS AS A BIOCHEMICAL MARKER
210
7601076 1986 DEC [15] JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY 15 (6): 1289-1291
PUIG L; MORENO A; NOGUERA X; DEMORAGAS JM
DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA WITH KERATOSIS PUNCTATA
00
770080 1987 APR [15] CLINICAL RESEARCH 35 (3): A702-A702
MCGUIRE J; BIRCHALL N; CUONO C; MOELLMANN G; KUKLINSKA E; et al.
SUCCESSFUL ENGRAFTMENT OF ALLOGENEIC KERATINOCYTE CULTURES IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
012
780081 1987 APR [15] JOURNAL OF INVESTIGATIVE DERMATOLOGY 88 (4): 506-506
MCGUIRE J; BIRCHALL N; CUONO C; MOELLMANN G; KUKLINSKA E; et al.
SUCCESSFUL ENGRAFTMENT OF ALLOGENEIC KERATINOCYTE CULTURES IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
29
790079 1987 JUN [15] BRITISH JOURNAL OF DERMATOLOGY 117: 68-69
NORRIS JFB; CUNLIFFE WJ
RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
00
8043478 1987 SEP [15] ARCHIVES OF OPHTHALMOLOGY 105 (9): 1248-1252
DESTRO M; WALLOW IHL; BRIGHTBILL FS
RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
410
#LCRNCRNode / Date / Journal / AuthorLCSGCS
811782 1987 NOV 16 MEDICAL JOURNAL OF AUSTRALIA 147 (10): 520-521
EISENBERG M; LLEWELLYN DM; MORAN K; KERR A
SUCCESSFUL ENGRAFTMENT OF CULTURED HUMAN EPIDERMAL ALLOGRAFT IN A CHILD WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
49
8212777 1987 DEC [15] ANESTHESIA AND ANALGESIA 66 (12): 1318-1320
KELLY RE; KOFF HD; ROTHAUS KO; CARTER DM; ARTUSIO JF
BRACHIAL-PLEXUS ANESTHESIA IN 8 PATIENTS WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
210
830086 1988 JAN [15] CLINICAL RESEARCH 36 (1): A58-A58
HAWKINS HK; EADY RAJ; LEVY ML; CARPENTER RC; HEJTMANCIK JF; et al.
PRENATAL-DIAGNOSIS OF DOMINANT DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
840087 1988 JAN [15] CLINICAL RESEARCH 36 (1): A84-A84
FINE JD; COUCHMAN J
19-DEJ-1 MONOCLONAL-ANTIBODY DEFINES A NEW SKIN BASEMENT-MEMBRANE ANTIGENIC DEFECT IN JUNCTIONAL AND DYSTROPHIC EPIDERMOLYSIS BULLOSA
06
850088 1988 JAN [15] CLINICAL RESEARCH 36 (1): A86-A86
TYRING SK; FINE JD
NATURAL-KILLER CELL-ACTIVITY IS DEPRESSED IN PATIENTS WITH JUNCTIONAL AND DYSTROPHIC EPIDERMOLYSIS BULLOSA BUT NOT IN PATIENTS WITH THE SIMPLEX FORM
01
8621792 1988 FEB [15] DERMATOLOGICA 176 (2): 57-64
BRUCKNERTUDERMAN L; RUEGGER S; ODERMATT B; MITSUHASHI Y; SCHNYDER UW
LACK OF TYPE-VII COLLAGEN IN UNAFFECTED SKIN OF PATIENTS WITH SEVERE RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
046
8721593 1988 FEB [15] DERMATOLOGICA 176 (2): 91-94
DERAEVE L; DEDOBBELEER G; SONG M; ACHTEN G
DOMINANT DYSTROPHIC EPIDERMOLYSIS BULLOSA OF COCKAYNE-TOURAINE IN FATHER AND SON - CLINICAL AND ULTRASTRUCTURAL SIMILARITIES
03
880983 1988 APR [15] ARCHIVES OF DERMATOLOGY 124 (4): 544-547
PEARSON RW; PALLER AS
DERMOLYTIC (DYSTROPHIC) EPIDERMOLYSIS BULLOSA INVERSA
812
890089 1988 APR [15] CLINICAL RESEARCH 36 (3): A375-A375
FINE JD; COUCHMAN J
19-DEJ-1, A HEMIDESMOSOME-ANCHORING FILAMENT COMPLEX-ASSOCIATED MONOCLONAL-ANTIBODY, DEFINES A NEW SKIN BASEMENT-MEMBRANE ANTIGENIC DEFECT IN JUNCTIONAL AND DYSTROPHIC EPIDERMOLYSIS BULLOSA
01
900090 1988 APR [15] CLINICAL RESEARCH 36 (3): A644-A644
FINE JD; COUCHMAN J
CHONDROITIN-6-SULFATE PROTEOGLYCAN BUT NOT HEPARAN-SULFATE PROTEOGLYCAN IS ABNORMALLY EXPRESSED IN SKIN BASEMENT-MEMBRANE FROM PATIENTS WITH DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
#LCRNCRNode / Date / Journal / AuthorLCSGCS
910091 1988 APR [15] CLINICAL RESEARCH 36 (3): A691-A691
RUSENKO KW; GAMMON WR; FINE JD; BRIGGAMAN RA
THE CARBOXYL-TERMINAL DOMAIN OF TYPE-VII COLLAGEN IS PRESENT IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
02
920097 1988 APR [15] JOURNAL OF INVESTIGATIVE DERMATOLOGY 90 (4): 558-558
FINE JD; COUCHMAN J
CHONDROITIN-6-SULFATE PROTEOGLYCAN BUT NOT HEPARAN-SULFATE PROTEOGLYCAN IS ABNORMALLY EXPRESSED IN SKIN BASEMENT-MEMBRANE FROM PATIENTS WITH DYSTROPHIC EPIDERMOLYSIS BULLOSA
10
930098 1988 APR [15] JOURNAL OF INVESTIGATIVE DERMATOLOGY 90 (4): 604-604
RUSENKO KW; CAMMON WR; FINE JD; BRIGGAMAN RA
THE CARBOXYL-TERMINAL DOMAIN OF TYPE-VII COLLAGEN IS PRESENT IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
11
94014102 1988 APR [15] PATHOLOGY 20 (2): 184-187
YI S; NAITO M; TAKAHASHI K; NOGAMI R; MAEKAWA Y; et al.
COMPLICATING SYSTEMIC AMYLOIDOSIS IN DYSTROPHIC EPIDERMOLYSIS BULLOSA, RECESSIVE TYPE
35
9582484 1988 MAY [15] ARCHIVES OF DERMATOLOGY 124 (5): 734-736
BAUER EA; TABAS M
A PERSPECTIVE ON THE ROLE OF COLLAGENASE IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
515
9631699 1988 MAY [15] JOURNAL OF INVESTIGATIVE DERMATOLOGY 90 (5): 639-642
LEIGH IM; EADY RAJ; HEAGERTY AHM; PURKIS PE; WHITEHEAD PA; et al.
TYPE-VII COLLAGEN IS A NORMAL COMPONENT OF EPIDERMAL BASEMENT-MEMBRANE, WHICH SHOWS ALTERED EXPRESSION IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
3094
97626101 1988 JUN [15] JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY 18 (6): 1246-1252
IKEDA S; MANABE M; MURAMATSU T; TAKAMORI K; OGAWA H
PROTEASE INHIBITOR THERAPY FOR RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA - INVITRO EFFECT AND CLINICAL-TRIAL WITH CAMOSTAT MESYLATE
23
9831085 1988 JUL [15] CLINICAL AND EXPERIMENTAL DERMATOLOGY 13 (4): 279-281
TIDMAN MJ; MARTIN IR; WELLS RS; MARSDEN RA; EADY RAJ
ESOPHAGEAL WEB FORMATION IN DYSTROPHIC EPIDERMOLYSIS BULLOSA
15
9900104 1988 JUL-SEP [JUL 15] TURKISH JOURNAL OF PEDIATRICS 30 (3): 187-191
KOCABAY K; GUVENC H; OKTEN A; BEKTAS S
A CASE OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
00
10051294 1988 SEP [15] DERMATOLOGICA 177 (3): 180-184
KEEFE M; WAKEEL RA; DICK DC
DEATH FROM METASTATIC, CUTANEOUS, SQUAMOUS-CELL CARCINOMA IN AUTOSOMAL RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA DESPITE PERMANENT INPATIENT CARE
813

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