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Fri Mar 10 15:15:24 2006
Papers with "Dystrophic Epidermolysis Bullosa" in the title

Nodes: 543, Authors: 1177, Journals: 123, Outer References: 2425, Words: 1041
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Collection span: 1952 - 2006
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#LCRNCRNode / Date / Journal / AuthorLCSGCS
201529201 1992 JOURNAL OF INVESTIGATIVE DERMATOLOGY 99 (5): 528-530
GRUIS NA; BAVINCK JNB; STEIJLEN PM; VANDERSCHROEFF JG; VANHAERINGEN A; et al.
GENETIC-LINKAGE BETWEEN THE COLLAGEN-VII (COL7A1) GENE AND THE AUTOSOMAL DOMINANT FORM OF DYSTROPHIC EPIDERMOLYSIS-BULLOSA IN 2 DUTCH KINDREDS
1228
2021039202 1992 JOURNAL OF INVESTIGATIVE DERMATOLOGY 99 (5): 550-558
BRUCKNERTUDERMAN L; WINBERG JO; ANTONLAMPRECHT I; SCHNYDER UW; GEDDEDAHL T
ANCHORING FIBRILS, COLLAGEN-VII, AND NEUTRAL METALLOPROTEASES IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA-INVERSA
711
203631203 1992 JOURNAL OF INVESTIGATIVE DERMATOLOGY 99 (6): 808-812
KONIG A; LAUHARANTA J; BRUCKNERTUDERMAN L
KERATINOCYTES AND FIBROBLASTS FROM A PATIENT WITH MUTILATING DYSTROPHIC EPIDERMOLYSIS-BULLOSA SYNTHESIZE DRASTICALLY REDUCED AMOUNTS OF COLLAGEN .7. LACK OF EFFECT OF TRANSFORMING GROWTH-FACTOR-BETA
713
204010204 1992 JOURNAL OF MEDICAL GENETICS 29 (6): 381-382
ALIMARA L; RICHARDS AJ; EADY RAJ; LEIGH IM; FARRALL M; et al.
LINKAGE OF AUTOSOMAL DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA IN 3 BRITISH FAMILIES TO THE MARKER D3S2 CLOSE TO THE COL7A1 LOCUS
1630
205511205 1992 NEW ENGLAND JOURNAL OF MEDICINE 327 (3): 163-167
CALDWELLBROWN D; STERN RS; LIN AN; CARTER DM
LACK OF EFFICACY OF PHENYTOIN IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
516
20600206 1992 PEDIATRIC DERMATOLOGY 9 (3): 231-238
ALLMAN S; HAYNES L; MACKINNON P; ATHERTON DJ
NUTRITION IN DYSTROPHIC EPIDERMOLYSIS-BULLOSA
611
20700207 1993 AMERICAN JOURNAL OF HUMAN GENETICS 53 (3): 1709-1709
POPE FM; ALIMARA L; EADY RAJ; DUNNILL G; RICHARDS AJ
ANCHORING FIBRIL PATTERNS ARE COMPATIBLE WITH LINKAGE OF ANONYMOUS AND COL7A1 MARKERS AT 3P21 IN 5 BRITISH FAMILIES WITH DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA
00
208216208 1993 AMERICAN JOURNAL OF MEDICAL GENETICS 47 (8): 1184-1188
WRIGHT JT; FINE JD; JOHNSON LB; STEINMETZ TT
ORAL INVOLVEMENT OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA-INVERSA
47
209332209 1993 ANAESTHESIA 48 (9): 810-815
GRIFFIN RP; MAYOU BJ
THE ANESTHETIC MANAGEMENT OF PATIENTS WITH DYSTROPHIC EPIDERMOLYSIS-BULLOSA - A REVIEW OF 44 PATIENTS OVER A 10-YEAR PERIOD
816
21005210 1993 ARCHIVES OF DERMATOLOGY 129 (9): 1212-1212
CHORNY JA; SHROYER KR; GOLITZ LE
MALIGNANT-MELANOMA AND A SQUAMOUS-CELL CARCINOMA IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
23
#LCRNCRNode / Date / Journal / AuthorLCSGCS
2112260211 1993 ARCHIVES OF DERMATOLOGY 129 (12): 1566-1570
HOVNANIAN A; CHRISTIANO AM; VITTO J
MOLECULAR-GENETICS OF DYSTROPHIC EPIDERMOLYSIS-BULLOSA
516
212930212 1993 BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS 193 (2): 604-610
IWASAKI T; LAPIERE JC; UITTO J; KIM YH; WOODLEY DT
RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA KERATINOCYTES SYNTHESIZE TYPE-VII COLLAGEN ALPHA-CHAINS OF NORMAL MOLECULAR-SIZE BUT THE ANCHORING FIBRIL ASSEMBLY IS IMPAIRED
07
21339213 1993 BRITISH JOURNAL OF DERMATOLOGY 128 (6): 708-709
DUNNILL MGS; MALLETT RB; HAWKINS PN; VALLANCE PJT; MARSDEN RA
SEVERE DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA COMPLICATED BY SYSTEMIC AMYLOIDOSIS
22
21416214 1993 BRITISH JOURNAL OF DERMATOLOGY 129 (4): 443-446
GOULDEN V; HANDFIELDJONES S; NEILD V; BLACK MM
LINEAR PRURIGO SIMULATING DERMATITIS ARTEFACTA IN DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA
04
215317215 1993 BRITISH JOURNAL OF DERMATOLOGY 129 (5): 602-605
ISHIKAWA O; WARITA S; OHNISHI K; MIYACHI Y
A SCLERODERMA-LIKE VARIANT OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
01
21603216 1993 BRITISH JOURNAL OF PLASTIC SURGERY 46 (3): 192-193
MULLETT FLH; SMITH PJ
HAND SPLINTAGE FOLLOWING SURGERY FOR DYSTROPHIC EPIDERMOLYSIS-BULLOSA
22
217025217 1993 BRITISH JOURNAL OF RADIOLOGY 66 (789): 788-793
WONG WL; ENTWISLE K; PEMBERTON J
GASTROINTESTINAL MANIFESTATIONS IN THE HALLOPEAU-SIEMENS VARIANT OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
14
21800218 1993 CLINICAL RESEARCH 41 (1): A39-A39
WANG M; UNEMORI E; RUDD R; MCGUIRE JS
TRANSFORMING GROWTH-FACTOR ALPHA UP-REGULATES TYPE-I COLLAGENASE PRODUCTION IN FIBROBLASTS FROM RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA PATIENTS
00
21900219 1993 CLINICAL RESEARCH 41 (2): A408-A408
CHRISTIANO AM; CHUNGHONET LC; GREENSPAN DS; UITTO J
CLONING AND CHARACTERIZATION OF HUMAN TYPE-VII COLLAGEN AND IDENTIFICATION OF A MISSENSE MUTATION IN 2 SIBLINGS WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA (RDEB)
00
22000220 1993 CLINICAL RESEARCH 41 (2): A409-A409
FINE JD; DANIELS A; ZENG L; CRONCE D; BRIGGAMAN R
COMPARATIVE-ANALYSIS OF THE SENSITIVITY AND SPECIFICITY OF ALTERED EXPRESSION OF ANCHORING FIBRILS AND TYPE-VII COLLAGEN FOR DIAGNOSIS AND SUBCLASSIFICATION OF DYSTROPHIC EPIDERMOLYSIS-BULLOSA SUBSETS
00
#LCRNCRNode / Date / Journal / AuthorLCSGCS
22100221 1993 CLINICAL RESEARCH 41 (2): A410-A410
HILLAL L; HOVNANIAN A; DUGUESNOY P; BLANCHETBARDON C; CHRISTIANO AM; et al.
CHARACTERIZATION OF MUTATIONS WITHIN THE TYPE-VII COLLAGEN GENE IN PATIENTS WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
00
22200222 1993 CLINICAL RESEARCH 41 (2): A410-A410
HOVNANIAN A; HILAL L; BLANCHETBARDON C; DOMMERGUES M; CONTEVILLE P; et al.
PRENATAL-DIAGNOSIS OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA BY ANALYSIS OF INTRAGENIC TYPE-VII COLLAGEN PVULL POLYMORPHISM
00
22300223 1993 CLINICAL RESEARCH 41 (2): A410-A410
IWASAKI T; LAPIERE JC; UITTO J; KIM YH; WOODLEY DT
RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA (RDEB) KERATINOCYTES SYNTHESIZE TYPE-VII (ANCHORING FIBRIL) COLLAGEN ALPHA-CHAINS OF NORMAL MOLECULAR-SIZE
00
22400224 1993 CLINICAL RESEARCH 41 (2): A431-A431
BRUCKNERTUDERMAN L; KONIG A; RAGHUNATH M; STEINMANN B
DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA - REDUCED NUMBER OF ANCHORING FIBRILS IS DUE TO INTRACELLULAR ACCUMULATION OF COLLAGEN-VII IN KERATINOCYTES
00
22500225 1993 CLINICAL RESEARCH 41 (2): A441-A441
KALINKE DU; KALINKE U; WINBERG IO; LAUHARANTA I; KONIG A; et al.
SEVERE RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA - EXPRESSION OF COLLAGEN-VII MESSENGER-RNA BUT LACK OF INTACT PROTEIN FROM SKIN AND CUTANEOUS CELLS
00
22600226 1993 CLINICAL RESEARCH 41 (2): A479-A479
KIM YH; KIM JP; CHEN JD; IWASAKI T; HERNANDEZ G; et al.
BIOLOGIC CHARACTERISTICS OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA (RDEB) KERATINOCYTES
00
22719227 1993 EUROPEAN JOURNAL OF PEDIATRIC SURGERY 3 (6): 352-355
LETOUZE A; VIAU D; MARTIN L; DEPONT P; ROBERT M
RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA - MANAGEMENT OF HAND DEFORMITIES
33
228937228 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (1): 93-96
JENISON M; FINE JD; GAMMON WR; OKEEFE EJ
NORMAL MOLECULAR-WEIGHT OF TYPE-VII COLLAGEN PRODUCED BY RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA KERATINOCYTES
12
2291145229 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 366-372
MCGRATH JA; ISHIDAYAMAMOTO A; OGRADY A; LEIGH IM; EADY RAJ
STRUCTURAL VARIATIONS IN ANCHORING FIBRILS IN DYSTROPHIC EPIDERMOLYSIS-BULLOSA - CORRELATION WITH TYPE-VII COLLAGEN EXPRESSION
4880
23000230 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 441-441
KALINKE DU; KALINKE U; WINBERG IO; LAUHARANTA I; KONIG A; et al.
EXPRESSION OF COLLAGEN-VII MESSENGER-RNA BUT LACK OF INTACT PROTEIN PRODUCT IN SKIN AND CUTANEOUS CELLS IN SEVERE RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
00
#LCRNCRNode / Date / Journal / AuthorLCSGCS
23100231 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 460-460
BRUCKNERTUDERMAN L; KONIG A; RAGHUNATH M; STEINMANN B
DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA - INTRACELLULAR ACCUMULATION OF COLLAGEN-VII IN KERATINOCYTES LEADS TO A REDUCED NUMBER OF ANCHORING FIBRILS AND SKIN BLISTERING
00
23200232 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 470-470
MCGRATH JA; ISHIDAYAMAMOTO A; OGRADY A; LEIGH IM; EADY RAJ
STRUCTURAL VARIATIONS OF ANCHORING FIBRILS IN DIFFERENT FORMS OF DYSTROPHIC EPIDERMOLYSIS-BULLOSA
00
23300233 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 499-499
HILAL L; HOVNANIAN A; DUQUESNOY P; BLANCHETBARDON C; CHRISTIANO AM; et al.
CHARACTERIZATION OF MUTATIONS WITHIN THE TYPE-VII COLLAGEN GENE IN PATIENTS WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
25
23400234 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 515-515
CHRISTIANO AM; CHUNGHONET LC; GREENSPAN DS; UITTO J
CLONING AND CHARACTERIZATION OF HUMAN TYPE-VII COLLAGEN AND IDENTIFICATION OF A MISSENSE MUTATION IN 2 SIBLINGS WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA (RDEB)
00
23500235 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 515-515
KALINKE DU; KALINKE U; WINBERG IO; LAUHARANTA I; KONIG A; et al.
SEVERE RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA - EXPRESSION OF COLLAGEN-VII MESSENGER-RNA BUT LACK OF INTACT PROTEIN FROM SKIN AND CUTANEOUS CELLS
00
23600236 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 515-515
IWASAKI T; LAPIERE JC; UITTO J; KIM YH; WOODLEY DT
RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA (RDEB) KERATINOCYTES SYNTHESIZE TYPE-VII (ANCHORING FIBRIL) COLLAGEN ALPHA-CHAINS OF NORMAL MOLECULAR-SIZE
00
23700237 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 515-515
HOVNANLAN A; HILAL L; BLANCHETBARDON C; DOMMERGUES M; CONTEVILLE P; et al.
PRENATAL-DIAGNOSIS OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA BY ANALYSIS OF INTRAGENIC TYPE-VII COLLAGEN PVULL POLYMORPHISM
03
23800238 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 532-532
FINE JD; DANIELS A; ZENG L; CRONCE D; BRIGGAMAN R
COMPARATIVE-ANALYSIS OF THE SENSITIVITY AND SPECIFICITY OF ALTERED EXPRESSION OF ANCHORING FIBRILS AND TYPE VII COLLAGEN FOR DIAGNOSIS AND SUBCLASSIFICATION OF DYSTROPHIC EPIDERMOLYSIS-BULLOSA SUBSETS
11
23900239 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 580-580
KIM YH; KIM JP; CHEN JD; IWASAKI T; HERNANDEZ G; et al.
BIOLOGIC CHARACTERISTICS OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA (RDEB) KERATINOCYTES
00
24000240 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 100 (4): 582-582
BRUCKNERTUDERMAN L; KONIG A; RAGHUNATH M; STEINMANN B
DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA - REDUCED NUMBER OF ANCHORING FIBRILS IS DUE TO INTRACELLULAR ACCUMULATION OF COLLAGEN-VII IN KERATINOCYTES
00
#LCRNCRNode / Date / Journal / AuthorLCSGCS
241716241 1993 JOURNAL OF INVESTIGATIVE DERMATOLOGY 101 (2): 232-236
FINE JD; JOHNSON LB; CRONCE D; WRIGHT JT; LEIGH IM; et al.
INTRACYTOPLASMIC RETENTION OF TYPE-VII COLLAGEN AND DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA - REVERSAL OF DEFECT FOLLOWING CESSATION OF OR MARKED IMPROVEMENT IN DISEASE-ACTIVITY
215
2421264242 1993 JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY 29 (3): 407-419
MCGRATH JA; SCHOFIELD OMV; ISHIDAYAMAMOTO A; OGRADY A; MAYOU BJ; et al.
CULTURED KERATINOCYTE ALLOGRAFTS AND WOUND-HEALING IN SEVERE RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
515
243435243 1993 NATURE GENETICS 4 (1): 62-66
CHRISTIANO AM; GREENSPAN DS; HOFFMAN GG; ZHANG X; TAMAI Y; et al.
A MISSENSE MUTATION IN TYPE-VII COLLAGEN IN 2 AFFECTED SIBLINGS WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
40117
2441546244 1993 NATURE GENETICS 5 (3): 287-293
HILAL L; ROCHAT A; DUQUESNOY P; BLANCHETBARDON C; WECHSLER J; et al.
A HOMOZYGOUS INSERTION-DELETION IN THE TYPE-VII COLLAGEN GENE (COL7A1) IN HALLOPEAU-SIEMENS DYSTROPHIC EPIDERMOLYSIS-BULLOSA
3178
245220245 1993 PRENATAL DIAGNOSIS 13 (1): 55-59
BASS HN; MIRANDA C; OEI R; CRANDALL BF
ASSOCIATION OF GENERALIZED DYSTROPHIC EPIDERMOLYSIS-BULLOSA WITH POSITIVE ACETYLCHOLINESTERASE AND MARKEDLY ELEVATED MATERNAL SERUM AND AMNIOTIC-FLUID ALPHA-FETOPROTEIN
02
2461346246 1994 AMERICAN JOURNAL OF HUMAN GENETICS 55 (2): 289-296
HOVNANIAN A; HILAL L; BLANCHETBARDON C; DEPROST Y; CHRISTIANO AM; et al.
RECURRENT NONSENSE MUTATIONS WITHIN THE TYPE-VII COLLAGEN GENE IN PATIENTS WITH SEVERE RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
2748
24707247 1994 ANNALS OF THORACIC SURGERY 57 (4): 1027-1029
HORAN TA; URSCHEL JD; MACEACHERN NA; SHULMAN B; CROWSON AN; et al.
ESOPHAGEAL-PERFORATION IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
02
24815248 1994 ARCHIVES OF DERMATOLOGY 130 (11): 1457-1458
CARROLL PB; RILO HLR; ABUELMAGD K; JOHNSON N; CARTER C; et al.
EFFECT OF TACROLIMUS (FK506) IN DYSTROPHIC EPIDERMOLYSIS-BULLOSA - RATIONALE AND PRELIMINARY-RESULTS
04
249745249 1994 BRITISH JOURNAL OF DERMATOLOGY 130 (5): 617-625
MCGRATH JA; SCHOFIELD OMV; EADY RAJ
EPIDERMOLYSIS-BULLOSA PRURIGINOSA - DYSTROPHIC EPIDERMOLYSIS-BULLOSA WITH DISTINCTIVE CLINICOPATHOLOGICAL FEATURES
1226
250526250 1994 BRITISH JOURNAL OF DERMATOLOGY 131 (4): 465-471
MCGRATH JA; SAKAI LY; EADY RAJ
FIBRILLIN IMMUNOREACTIVITY IS ASSOCIATED WITH NORMAL OR FRAGMENTED ELASTIC MICROFIBRILS AT THE DERMAL-EPIDERMAL JUNCTION IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
14
#LCRNCRNode / Date / Journal / AuthorLCSGCS
2511436251 1994 EUROPEAN JOURNAL OF DERMATOLOGY 4 (6): 463-470
WINBERG JO; ANTONLAMPRECHT I; KONIG A; BRUCKNERTUDERMAN L; NILSSEN O; et al.
BIOCHEMICAL, MOLECULAR AND ULTRASTRUCTURAL HETEROGENEITY IN SEVERE MUTILATING RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
04
252419252 1994 EUROPEAN JOURNAL OF DERMATOLOGY 4 (7): 553-557
SUGA Y; ISHIDOH K; MANABE M; MORIOKA S; TAKAMORI K; et al.
PCR-SSCP ANALYSIS OF TYPE-VII COLLAGEN GENE MUTATION IN DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA
11
253740253 1994 EXPERIMENTAL CELL RESEARCH 211 (2): 212-218
UNEMORI EN; MAUCH C; HOEFFLER W; KIM Y; AMENTO EP; et al.
CONSTITUTIVE ACTIVATION OF THE COLLAGENASE PROMOTER IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA FIBROBLASTS - ROLE OF ENDOGENOUSLY ACTIVATED AP-1
17
254840254 1994 GENOMICS 21 (1): 160-168
CHRISTIANO AM; ANHALT G; GIBBONS S; BAUER EA; UITTO J
PREMATURE TERMINATION CODONS IN THE TYPE-VII COLLAGEN GENE (COL7A1) UNDERLIE SEVERE, MUTILATING RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
4277
255613255 1994 HUMAN MOLECULAR GENETICS 3 (9): 1693-1694
DUNNILL MGS; RICHARDS AJ; MILANA G; MOLLICA F; EADY RAJ; et al.
A NOVEL HOMOZYGOUS POINT MUTATION IN THE COLLAGEN-VII GENE (COL7A1) IN 2 COUSINS WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
2126
256641256 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 102 (1): 105-110
KONIG A; RAGHUNATH M; STEINMANN B; BRUCKNERTUDERMAN L
INTRACELLULAR ACCUMULATION OF COLLAGEN-VII IN CULTURED KERATINOCYTES FROM A PATIENT WITH DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA
215
257936257 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 102 (2): 155-159
KONIG A; WINBERG JO; GEDDEDAHL T; BRUCKNERTUDERMAN L
HETEROGENEITY OF SEVERE DYSTROPHIC EPIDERMOLYSIS-BULLOSA - OVEREXPRESSION OF COLLAGEN-VII BY CUTANEOUS CELLS FROM A PATIENT WITH MUTILATING DISEASE
210
258318258 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 102 (2): 260-262
KALINKE DU; KALINKE U; WINBERG JO; KONIG A; LAUHARANTA J; et al.
COLLAGEN-VII IN SEVERE RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA - EXPRESSION OF MESSENGER-RNA BUT LACK OF INTACT PROTEIN PRODUCT IN SKIN AND CUTANEOUS CELLS IN-VITRO
05
25900259 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 102 (4): 559-559
UITTO J; HOVNANIAN A; CHRISTIANO AM
HETEROGENEITY OF MUTATIONS IN THE TYPE-VII COLLAGEN GENE IN DIFFERENT FORMS OF RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA (RDEB) - PREMATURE TERMINATION CODONS (PTC) VS MISSENSE MUTATIONS
00
26000260 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 102 (4): 559-559
CHRISTIANO AM; RYYNANEN M; UITTO J
DOMINANT DYSTROPHIC EPIDERMOLYSIS-BULLOSA (DDEB) RESULTS FROM A GLYCINE SUBSTITUTION IN THE TRIPLE-HELICAL DOMAIN OF THE TYPE-VII COLLAGEN GENE (COL7A1)
00
#LCRNCRNode / Date / Journal / AuthorLCSGCS
26100261 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 102 (4): 621-621
CIATTI S; CHRISTIANO AM; PARADISI M; MORRICONE A; ANGELO C; et al.
RECURRENT PREMATURE TERMINATION CODON MUTATION IN THE TYPE-VII COLLAGEN GENE (COL7A1) IN 2 FAMILIES WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA IN ITALY
00
26200262 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 102 (4): 623-623
DUNNILL MGS; RICHARDS AJ; MILANA G; ALIMARA L; EADY RAJ; et al.
GENETIC-LINKAGE TO THE TYPE-VII COLLAGEN GENE IN 25 FAMILIES WITH GENERALIZED RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
00
26300263 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 103 (2): 272-272
LIN A; SMITH LT; FINE JD
INVERSE DYSTROPHIC EPIDERMOLYSIS-BULLOSA - REPORT OF 2 CASES WITH FURTHER CORRELATION BETWEEN IMMUNOFLUORESCENCE STUDIES AND ELECTRON-MICROSCOPY
00
26400264 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 103 (3): 406-406
BRUCKNERTUDERMAN L; ZIMMERMANN D; ZIMMERMANN MT; WINBERG JO; KALINKE U; et al.
LACK OF PROCESSING OF PROCOLLAGEN-VII TO COLLAGEN-VII UNDERLIES DYSTROPHIC EPIDERMOLYSIS-BULLOSA IN SOME PATIENTS
00
26500265 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 103 (3): 438-438
DUNNILL MGS; RICHARDS AJ; MILANA G; MOLLICA F; EADY RAJ; et al.
A POINT MUTATION OF THE TYPE-VII COLLAGEN GENE (COL7A1) IN 2 COUSINS AND 3 UNRELATED PATIENTS WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
00
26600266 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 103 (6): 845-845
CHRISTIANO AM; SUGA Y; HOVNANIAN A; GREENSPAN DS; OGAWA H; et al.
PREMATURE TERMINATION CODONS ON BOTH ALLELES OF THE TYPE-VII COLLAGEN GENE (COL7A1) IN 3 JAPANESE BROTHERS WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
00
26701267 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 103 (6): 845-845
DUNNILL MGS; LEVENE GM; MCKEE PH; MAYOU BJ; EADY RAJ
DYSTROPHIC EPIDERMOLYSIS-BULLOSA COMPLICATED BY SQUAMOUS-CELL CARCINOMA - WORTH A 2ND LOOK
00
26800268 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 103 (6): 849-849
HOVNANIAN A; HILAL L; BLANCHETBARDON C; DEPROST Y; CHRISTIANO AM; et al.
RECURRENT NONSENSE MUTATIONS WITHIN THE TYPE-VII COLLAGEN GENE IN PATIENTS WITH SEVERE RECESSIVE DYSTROPHIC EPIDERMOLYSIS-BULLOSA
01
26900269 1994 JOURNAL OF INVESTIGATIVE DERMATOLOGY 103 (6): 850-850
KOSSHARNES D; ANTONLAMPRECHT I; BRUCKNERTUDERMANN L; GEDDEDAHL T
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